Management of Pulmonary Arteriovenous Malformations

Abstract

Pulmonary arteriovenous malformations are rare lesions with significant clinical complications. These lesions are commonly seen in patients with hereditary hemorrhagic telangiectasia (formerly Osler-Weber-Rendu syndrome). Interventional radiologists are a key part of the treatment team in this complex disease, and a thorough understanding of the disease process is critical to providing good patient care. In this article, the authors review the disease course and its association with hereditary hemorrhagic telangiectasia, discusses the clinical evaluation and treatment of these complex patients, and outlines complications and follow-up.

Giant Sporadic Pulmonary Arteriovenous Malformation

“…However, transarterial embolization is usable as an effective method for PAVM treatment today (1,4,6,12). The studies are reporting recanalization and the need for re-treatment in 5-17% ratio after transarterial embolization, in the literature.…”

“…Although PAVM is usually combined with hereditary hemorrhagic telangiectasia, it rarely seen as sporadic (1). A case of PAVM is presented with radiological findings and the literature data.…”

“…Pulmonary arteriovenous malformation (PAVM) is a rare clinical entity that can lead to emergency clinical situations such as bleeding, pneumothoraks and the long-term chronic hypoxic problems due to right-to-left shunt (1,2). Although PAVM is usually combined with hereditary hemorrhagic telangiectasia, it rarely seen as sporadic (1).…”

Cyanosis Skipped Till 11 Years of Age

“…Literatürde bu hastalar genellikle olgu sunumları şeklinde yer aldığından bu hastaların tanı, tedavi ve takiplerinde ortak bir görüş birliği yoktur. Ancak endovasküler girişimlerin ve kullanılan cihazların gelişmesi ile birlikte bu gün için en çok tercih edilen tedavi yöntemi kateter yoluyla yapılan embolizasyondur (8,9). Özellikle arteriyovenöz malformasyonu besleyen bir kaç adet afferent arter var ve bunlara kateter yoluyla ulaşılabiliyorsa embolizasyon tercih edilmelidir (8,9).…”

Pulmonary Arteriovenous Malformations: Current Technique of Transcatheter Embolization and Subsequent Management

“…In the anchor technique, the coil tip is purposely anchored in a small side-branch proximal to the fistulous point of the PAVM, and the body of the coil then prolapses into the feeding artery. By securing the tip in a side branch, the risk of inadvertent coil dislodgment is minimized [18]. In the scaffold technique, the first positioned coil creates a scaffold and permits the blockage of other devices.…”