Maxillary Acanthomatous Ameloblastoma With Orbital Involment - A Rare Clinical Variant

Abstract

Ameloblastoma is a group of rare benign odontogenic tumour, accounting for around 1% of all the cysts and tumours in the jaw. Predominantly this tumour occurs in the mandible and rarely crosses the midline. The typical clinical presentation is that of facial dysmorphism and functional dysfunction due to the expansile and compressive nature of the tumour. Of the six histological subtypes described, Acanthomatous variant is relatively very rare. A Large ameloblastoma with acanthomatous variant of maxilla is also unusual. This case discusses the diagnostic and therapeutic challenges in the management of a large maxillary acanthomatous ameloblastoma that had extended into the orbit, ethmoids and sphenoid sinus.