Median Cleft of Lower Lip and Mandible, Cleft Sternum and Absence of Basihyoid

Morton, Charles Bruce; Jordan, H. E.

doi:10.1001/archsurg.1935.01180100093010

Cited by 49 publications

(28 citation statements)

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“…Tractions performed by these fibrous bands on the lower part of the mandibular symphysis can generate a bony spur seen on X-rays [16,17]. Associated pathologies are reported in the literature though none was noted in our series: cleft of the lower lip, of the tongue, of the mandible, of the sternum or hypoplasia of median structures such as hyoid bone [2]. Complete aplasia of hyoid bone and thyroid cartilage has also been reported by Morton and Jordan [2].…”

Section: Discussionmentioning

confidence: 75%

“…Developmental anomalies of branchial arches can provoke several malformations. The main theory hypothesized that midline clefts are the consequence of an anterior fusion defect of the two first pairs of branchial arches during the third and fourth weeks of intra-uterine life [2,[9][10][11]. However, Gargan proposed several hypothesis: defect of splitting of the ectoderm from epimyocardial mesoderm and anterior part of first branchial arch, vascular malformations leading to localized ischemia and necrosis [12].…”

Section: Discussionmentioning

confidence: 99%

“…However, Gargan proposed several hypothesis: defect of splitting of the ectoderm from epimyocardial mesoderm and anterior part of first branchial arch, vascular malformations leading to localized ischemia and necrosis [12]. Pressure of primitive heart on branchial arches could generate adhesions and provoking a defect of fusion between them [2]. Bergevin et al [9] hypothesized that an added formation was developed from first branchial arch mesoderm.…”

Section: Discussionmentioning

confidence: 99%

“…Congenital midline cervical cleft is clinically typical [1][2][3][4][5][6][7][8][9][10][11][13][14][15][16][17][18][19][20][21][22] and diagnosed at birth. Length and width can differ from one child to another but clinically cleft presents as linear vertical areas of thin and erythematous skin.…”

Section: Discussionmentioning

confidence: 99%

“…They were first described by Luschka [1] in 1848. Morton and Jordan [2] published in 1935 the fourth case of congenital midline cervical cleft which extended from the lower lip to the manubrium with absence of hyoid bone. This malformation was completely described by Ombredanne [3] in his book of pediatric surgery in 1946.…”

Section: Introductionmentioning

confidence: 99%

See 4 more Smart Citations

Congenital midline cervical cleft of the neck: a series of five cases

Derbez

Nicollas

Roman

et al. 2004

International Journal of Pediatric Otorhinolaryngology

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Section: Discussionmentioning

confidence: 75%

Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

Section: Introductionmentioning

confidence: 99%

See 3 more Smart Citations

Congenital midline cervical cleft of the neck: a series of five cases

Derbez

Nicollas

Roman

et al. 2004

International Journal of Pediatric Otorhinolaryngology

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Multiple congenital anomalies in a stillborn infant

Ashley

Richardson

1943

Anat. Rec.

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Cleft sternum: Case report and brief commentary

Knight¹,

Morley²

1936

Journal of British Surgery

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COMPLETE median cleft or fissure of the sternum has been described by various observers, usually associated with defects of the neck and abdominal wall. The authors feel that the case to be described here, having no detectable abnormality other than the sternal deficiency and a superficial scar of the abdominal wall, is therefore worthy of record. HISTORICAL SURVEYGibson and Malet1 (1879) described a case in which a sternal fissure existed in the cranial end of the bone as far downwards as the upper border of the fourth rib ; this was associated with a strong membrane attaching the sternal edge in the cleft to the cricoid cartilage, and a scar-like strip of skin, 3 in. long, passing upwards from the umbilicus. Professor Sir William Turner2 (I 879) described a specimen in the Anatomical Museum of the University of Edinburgh, with fissure of the sternum ending at the level of the seventh rib, where the two halves articulated in the mid-line. He quoted cases of Herr Groux, Skoda and Forster, the former describing, apparently, his own condition, and the latter found the ribs to be fused to the sternum without articulation. Martin3 (1887) described a case in a new-born female, which he traced to be healthy to the age of 4& months, though with umbilical hernia, divarication of the rectus muscles, and attenuation of the skin of the precordial area.More recently Barillet4 described a case in which the cleft was sufficiently large to permit examination and direct record of the aortic pulse. Benhamou, Hermann, and Levi-Valensij have described a case of apparent complete absence, as opposed to fissure, of the sternum, with records of cardiograms obtained directly through skin from the pericardial surface of the heart as far out as the apex. It is interesting to note that no cardiac abnormality could be detected.The condition was exhaustively reviewed in 1922 by Alfred Szenes6 and in 1926 by Mr. David Greig, of Edinburgh.' Szene's case was a male aged 8 years, with complete fissure of the manubrium and body of the sternum as far as the xiphoid at the sixth costal cartilages. Scarred skin lined the fissure and a ligamentous raphe connected a spur-like protuberance of the chin with the sternal fissure, over which it spread fan-wise. This raphe caused a pouch-like fullness of the neck and limited extension of the head on the neck.Morton and JordanY (1935) described a still further stage in a case of median cleft of the lower lip and mandible, cleft sternum, and absence of the basi-hyoid. In their case the sternal deformity consisted of apparent absence of the manubrium and upper half of the sternum, with the inferior gnathoschisis and the connecting area of scar tissue from the mental region to the floor of the sternal cleft.

show abstract

Median Cleft of Lower Lip and Mandible, Cleft Sternum and Absence of Basihyoid

Cited by 49 publications

References 1 publication

Congenital midline cervical cleft of the neck: a series of five cases

Congenital midline cervical cleft of the neck: a series of five cases

Multiple congenital anomalies in a stillborn infant

Cleft sternum: Case report and brief commentary

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