Mediastinal and pulmonary infantile myofibromatosis: an unusual surgical presentation

Short, Melissa; Dramis, Asterios; Ramani, Pramila; Parikh, Dakshesh

doi:10.1016/j.jpedsurg.2008.06.046

Cited by 13 publications

(9 citation statements)

References 14 publications

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“…A single case of infantile myofibromatosis with multifocal masses in the lung and mediastinal soft tissue in a 4-week-old male infant has been reported. Five years after surgical resection and pneumonectomy, no disease activity was recorded [ 205 ].…”

Section: Fibroblastic/myofibroblastic Tumoursmentioning

confidence: 99%

Mesenchymal tumours of the mediastinum—part I

et al. 2015

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The mediastinum is an anatomically defined space in which organs and major blood vessels reside with surrounding soft tissue elements. The thymus is an important organ in the mediastinum, and many of the masses encountered in the mediastinum are related to this organ. Most neoplasms diagnosed in the mediastinum are epithelial tumours (thymomas and thymic carcinomas), lymphomas or germ cell tumours. In contrast, soft tissue tumours of the mediastinum are rare. In 1963, Pachter and Lattes systematically reviewed soft tissue pathology of the mediastinum, covering the hitherto described [2, 226, 227] In this review, based on the 2013 WHO classification of soft tissue tumours and the 2015 WHO classification of tumours of the lung, pleura, thymus and heart, we provide an updated overview of mesenchymal tumours that may be encountered in the mediastinum.

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Section: Fibroblastic/myofibroblastic Tumoursmentioning

confidence: 99%

Mesenchymal tumours of the mediastinum—part I

et al. 2015

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“…A single case of (infantile) myofibromatosis, which in the WHO classification is included in the spectrum of pericytic tumours, located in the central mediastinum and involving the hilar region of the lung was described in a 4-year-old male infant and was treated by pneumonectomy [ 181 ].…”

Section: Pericytic (Perivascular) Tumoursmentioning

confidence: 99%

Mesenchymal tumours of the mediastinum—part II

et al. 2015

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“…In addition to interferon‐alpha treatment, there are some other options such as chemotherapy, radiation, and surgical excision . When the viscera are not involved, treatment is usually not recommended because of the tendency toward spontaneous regression.…”

Section: Discussionmentioning

confidence: 99%

“…However, radical surgical excision may be required if vital organs are involved or if lesions are symptomatic. Short et al reported a case of a 4‐week‐old patient who was treated with left pneumonectomy for the left lung myofibromatosis. In our case, tumor excision was performed with no need for major lung resection.…”

Section: Discussionmentioning

confidence: 99%