Melanotic neuroectodermal tumor of infancy. Case Report.

Abstract

This case report presents the epidemiology, symptomathology, pathogenesis and treatment of a melanotic neuroectodermal tumour of infancy. MNTI is a rare tumour that is seen usually at or around birth. It is usually localised in facial region. The tumour originated from medial part of alveolar process of maxilla. Presented case developed in maxilla of four months old girl. Excision of a tumour with a dental germ 61 was performed. Despite MNTI shows benign hystological character it has a high recurrence potential. Two months after first operation during routine follow up control, there was a tumour in oral cavity that was suspected to be relapse. Patient undergone second prodecure in general anesthesia. Tumour was excised with radical margins. Due to complex funcitional and aesthetic character of facial region patients need specialistic treatment and rehabilitation of masticatory organ. Frequent presence of dental germs in the mass of tumour often causes malocclusion.

Early Class III Treatment Using a Hybrid Rapid Palatal Expander and Facemask in a Patient with Partially Edentulous Maxilla Post MNTI Removal: A Case Report

“…Surgery is in all cases, the treatment of first choice, and involves radical resection of the tumour until disease-free tissue margins are obtained. In fact, relapses are associated with non-radical surgery [ 17 ].…”

“…Recurrences are estimated in the literature to be around 20% and 25% [ 17 ]. This kind of recurrence risk, which is high, together with the rapid expansion of the tumour in the first few months of life, necessitates extensive surgical resections with extraoral access routes.…”