Melorreostosis: presentación de un caso y revisión de la literatura

Monte, T. C. Salman; Sala, Delfi Rotés; Rubió, Josep Blanch; Bittermann, Violeta; Abelló, Jordi Carbonell

doi:10.1016/j.reuma.2010.11.007

Cited by 9 publications

(4 citation statements)

References 7 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…However, on many occasions we need a bone biopsy or bone gammagraphy to discount pathologies which affect bone metabolism. The initial diagnosis was not totally uncertain given that in Paget's disease, in response to bone resorption, there is an increase in bone formation, resulting in an increase in the thickness of some trabeculae and an irregular hypertrophy of the trabecular bone 7 . As a consequence, the bone marrow is infiltrated with an excess of fibrous connective tissue and of blood vessels which lead to hypervascularisation, findings which are compatible with melorheostosis where the cortical hyperostosis causes thickening and trabecular bone and vascular increase.…”

Section: Discussionmentioning

confidence: 99%

“…The diagnosis is usually carried out through diagnostic imaging techniques, notable among which is simple radiography 5 . With this we may observe an image which resembles "wax dripping down the side of a candle", a sign which gives us a secure diagnosis in most cases 6,7 . The treatment is mainly symptomatic, and only occasionally requires recourse to surgery.…”

Section: Introductionmentioning

confidence: 88%

See 1 more Smart Citation

Melorreostosis: presentación de un caso clínico

Bordón

González

Borbones

et al. 2015

Rev Osteoporos Metab Miner

View full text Add to dashboard Cite

Melorheostosis is a form of hyperostosis which affects both bone and the adjacent soft tissues. Its incidence is variable, although it is higher in the second and third decades of life due to the slowly progressive nature of the disease. It generally presents with pain which may cause significant functional limitation. We may be assisted in its diagnosis by its characteristic radiological image which resembles "wax melting down the side of a candle". A case of melorheostosis is presented with clinical findings and radiological characteristics. The patient had previously been diagnosed with Paget's disease of bone, so we proposed a differential diagnosis of this pathology.

show abstract

Section: Discussionmentioning

confidence: 99%

Section: Introductionmentioning

confidence: 88%

Melorreostosis: presentación de un caso clínico

Bordón

González

Borbones

et al. 2015

Rev Osteoporos Metab Miner

View full text Add to dashboard Cite

show abstract

“…Patients commonly present with pain, deformities, limitations of a range of motion, contractures, muscle atrophy, and limb swelling [5]. Most cases were diagnosed incidentally and may involve different skeletal regions such as vertebrae, sternum, or upper and lower extremities, with the lower limbs being the most affected [1,[6][7]. Complications such as trigger finger or carpal tunnel syndrome, along with joint stiffness causing motion range limitation and deformities, could develop due to soft tissue swelling and fibrosis.…”

Section: Introductionmentioning

confidence: 99%

A Rare Case of Melorheostosis in the Hand of a Saudi Woman

Abed

Mashrah

Almahdaly

et al. 2020

Cureus

View full text Add to dashboard Cite

Melorheostosis is a very rare bone dysplasia, especially in the hand. Most cases were diagnosed incidentally, with the lower limbs being the most affected. This is the first Saudi woman with hand melorheostosis. A 33-year-old Saudi female had mild to moderate right-hand pain that started six years ago. Hand examination showed a full range of motion and full hand grip, and there was no tenderness upon palpation. Plain X-ray, unenhanced CT scan, and MRI of the hand showed an appearance resembling dripping candle wax as melorheostosis. The bone scan showed a nonvascular and nonacute lesion. An unenhanced CT scan demonstrated cortical and endosteal hyperostosis involving the proximal, middle, and distal third and fourth phalanges. Multisequential MRI of the hand demonstrated cortical hyperostosis involving the ulnar and radial aspect of the right fourth proximal, middle, and distal phalanges. Features in the X-ray, CT scan, bone scan, and MRI confirmed a diagnosis of melorheostosis with associated flexor tenosynovitis.

show abstract

“…It has a peculiar radiological characteristic, i.e. cortical thickening resembling "melted candle wax" ( 1 - 3 ) . Both female and male individuals are equally affected.…”

mentioning

confidence: 99%