We report the rare case of a 54-year-old man with uncontrolled renovascular hypertension, who was found to have an abdominal aortic aneurysm with congenital solitary pelvic kidney and superior mesenteric artery stenosis. A single renal artery branched from aneurysmal aortic bifurcation, and both the renal artery and the superior mesenteric artery (SMA) had severe stenosis at their origins. The aneurysm was repaired with a bifurcated Dacron graft, to which the renal artery was anastomosed. SMA bypass was created between the graft's left limb and the SMA using another Dacron graft. The operation was successful, with improvement in renal functions and control of hypertension.
Keywords: abdominal aortic aneurysm, congenital solitary pelvic kidney, renovascular hypertension
Case ReportA 54-year-old man was referred to our hospital with the diagnosis of AAA, and he presented with renovascular hypertension, renal anemia, and impaired renal function. He was 170 cm tall and weighed 54 kg. His hypertension was uncontrolled despite receiving daily doxazosin (alpha blocker) 4 mg, and nifedipine 80 mg. He has been a tobacco smoker for more than 40 years (20 cigarettes a day). He had no surgical history. Preoperative multidetector computed tomography (MDCT) scan showed a fusiform AAA with a maximum diameter of 45 mm, and a functioning congenital solitary pelvic kidney (Fig. 1A). A single renal artery branched from the aneurysmal aortic bifurcation, which showed 90% stenosis at its origin (Fig. 1B). The renal vein drained directly into the inferior vena cava. With regard to preoperative kidney function, serum creatinine level was 2.65 mg/dl, creatinine clearance rate was 30 ml/min, technetium-99m-mercaptoacetylglycylglycylglycine ( 99m Tc-MAG) clearance rate was 52.8 ml/min, hemoglobin level was 11.5 g/dl, and serum renin level was 6.6 ng/ml/hr. Additionally, the superior mesenteric artery (SMA) showed 70% stenosis at its origin, but without abdominal symptoms (Fig. 1A).Open repair of AAA was performed. In the abdominal cavity, there were no anomalies other than the solitary pelvic kidney. During aortic clamping, renal flow was maintained with a temporary bypass between the right brachial and renal arteries by using Brewster's method ( Fig. 2A). 2)