Metastatic Malignant Chondroid Syringoma: A Rare Case Scenario

Abstract

Background: Malignant chondroid syringoma is one of the rarest clinical entities. It is a mixed cutaneous tumor with propensity for local invasion resulting in multiple local recurrences. Malignant chondroid syringoma has female predilection common in extremities. We are presenting this case in view of its rare presentation among the population, and unique clinical course. Case Report: A 38-year-old lady, known case of malignant chondroid syringoma of the left hand was treated for multiple local recurrences with excision, local radiation therapy and chemotherapy. She developed distant visceral metastasis over a span of 20 years after the primary diagnosis. Conclusion: Malignant chondroid syringoma has potential for both local recurrence and distant metastasis over a prolonged clinical course with on and off remission period. Because of its longer clinical course patients are recommended to be on regular follow up.