Metastatic Peripheral Primitive Neuroectodermal Tumor (PNET) Masquerading As Liver Abscess

Hyun, Chris B.; Lee, Y.; Bemiller, Timothy

doi:10.1097/00004836-200207000-00020

Cited by 21 publications

(19 citation statements)

References 23 publications

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“…Bone invasion and extraorbital extension have been described in the published cases of orbital pPNET,8 9 13 15 17 but only two cases showed systemic metastases,7 10 and regional lymph-node involvement was found in another case 17. None of the two cases with systemic metastases showed local bone invasion or extraorbital extension.…”

Section: Discussionmentioning

confidence: 95%

Peripheral primitive neuroectodermal tumour of the orbit

Romero

Castano²,

Abelairas

et al. 2010

British Journal of Ophthalmology

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Peripheral primitive neuroectodermal tumours (pPNETs) are a group of soft-tissue tumours of neuroepithelial origin that arise outside the central and sympathetic nervous system. Orbital location is infrequent, and to the best of the authors' knowledge only 16 cases have been reported in the literature. With this article, the authors report the demographics and clinical characteristics, diagnostic features, differential diagnosis, prognosis and therapeutic options of primary orbital peripheral primitive neuroectodermal tumour, based on their patients and on the cases reported in the literature to date. A differential diagnosis should be made with other small round cell tumours; immunohistochemical and ultrastructural techniques are essential for this purpose. Although bone invasion and extraorbital extension are possible, systemic metastases are uncommon in the cases of orbital pPNETs. Surgery has been the initial treatment in most cases; chemotherapy with or without radiotherapy is considered the best additional treatment. The orbital pPNET could be less aggressive than other forms of pPNETs, since most of the patients reported were alive after the follow-up period (at least 6 months).

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Section: Discussionmentioning

confidence: 95%

Peripheral primitive neuroectodermal tumour of the orbit

Romero

Castano²,

Abelairas

et al. 2010

British Journal of Ophthalmology

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“…Involvement of visceral organs by PNET is particularly rare. Involvement of the liver has been reported in the form of metastasis from other primary sources [116,117]. There are only a few cases of primary hepatic neuroectodermal tumor reported worldwide in the literature [118,119].…”

Section: Primary Primitive Neuroectodermal Tumormentioning

confidence: 99%

Rare hepatic malignant tumors: dynamic CT, MRI, and clinicopathologic features: with analysis of 54 cases and review of the literature

Tan

Xiao

2012

Abdom Imaging

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“…Os pPNETs são tumores que progridem rapidamente e geralmente, apresentam mau prognóstico (2) . Quando localizados na órbita podem comprometer os ossos locais, metástases sistêmi-cas, entretanto, são raras, havendo 2 casos descritos na literatura (2,12) cujos sítios foram pulmão e fígado. De forma semelhante, as recidivas não são freqüentes tendo ocorrido em 3 casos (2,5,8) .…”

Section: Discussionunclassified