Monophasic Synovial Sarcoma of the Lower Eyelid: Rare Tumor involving Rare Site

Abstract

Aim: Synovial sarcoma of eyelid is extremely rare. We are reporting a case of massive synovial sarcoma of lower eyelid extending to soft tissues over the anterior wall of maxilla. Case report:A 58-year-old male patient presented with a large mass involving the left lower eyelid and extending over the soft tissues of the anterior wall of the maxilla since 15 years. Clinical examination showed a firm soft tissue mass measuring 16 × 8 × 6 cm involving the left lower eyelid and extending to soft tissues over the maxilla. The mass showed ulceration and was bleeding on touch.Computed tomography scan showed an exophytic lobulated heterogeneously enhancing mass lesion with intense enhancing capsule measuring 14 × 9.3 × 8.4 cm with few internal areas of necrosis arising from left preseptal region. The lesion was causing erosion at the medial wall and floor of left orbit.It was clinically diagnosed as hemangiopericytoma. The patient was taken up for surgery and wide excision of the tumor and medial maxillectomy was done. The defect was reconstructed with a glabellar flap.