Introduction Larrey hernia is a very rare type of the left sided parasternal congenital hernia with the incidence of 1-3% of all anterior diaphragmatic hernias. Case report The paper describes Larrey congenital diaphragmatic hernia in an adult female patient, aged 70 years. Seventeen years earlier, the patient had had problems with intermittent left side chest pain, hypertension, dyspnea, shortness of breath, fatigue, and abdominal discomfort. She had no past surgical history, and no traumatic rupture of the diaphragm. An open surgical repair was conducted, reducing the herniated organs back into the abdominal cavity, and closing the diaphragmatic defect, repaired with a non-absorbable suture. During the immediate postoperative period, as well as six months later, the patient had a remarkable postoperative recovery. Conclusion Larrey hernia represents an extremely rare kind of the anterior diaphragm hernias, which can be symptomatically manifested in older persons over 65 years of age. The treatment in the cases of asymptomatic and symptomatic Larrey hernias is a surgical intervention.