Multimodality Imaging in an Adult Patient with Scimitar Syndrome

Abstract

The “Scimitar syndrome” is a rare congenital anomaly characterized by combination of partial or complete pulmonary venous return from the right lung to the inferior vena cava either above or below the diaphragm together with hypoplasia of the right lung and sometimes systemic arterial supply to the right lung. In this case, multimodality imaging findings such as the vein draining into the inferior vena cava, the presence of hypertrophied and dilated right ventricle, the absence of other cardiac abnormalities, displacement of the heart without malrotation and the mediastinum to the right, normal bronchial and vascular continuity in the whole lung, absence of pulmonary sequestration and systemic collaterals, normal perfusion and systolic functions of the left ventricle were reported.

Síndrome da Cimitarra em paciente com Linfoma não-Hodgkin: relato de caso

“…Embora o tratamento cirúrgico da Síndrome da Cimitarra seja controverso, a ressecção parcial ou total do pulmão direito, a divisão do suprimento arterial anormal para o pulmão direito ou o redirecionamento da veia da cimitarra para o átrio esquerdo podem ser opções de tratamento eficazes (KARAÇALIOĞLU et al, 2014).…”

Incidental detection of a curved radiopacity on the chest X-ray

“…[23] Infantile patients present with respiratory insufficiency and cardiac failure while adult patients are usually asymptomatic or present with repeat episodes of infection, minor dyspnea, or hemoptysis. [4]…”

Artifacts and Anatomical Variants Affecting Ventilation and Perfusion Lung Imaging

“…51,52 Although this usually drains the entire lung, in one-third, the scimitar veins drain only the lower portion of the right lung. 53 The example shown is of a 56-year-old woman who presented with pleuritic chest pain. She initially had a chest X-ray performed, which showed a normal result, and then proceeded to a planar V/Q scan (Fig.…”