Multiple koenen tumors: An uncommon presentation

Devi, Basanti; Dash, Manjulata; Behera, Binodini; Puhan, Manas Ranjan

doi:10.4103/0019-5154.91855

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Cited by 4 publications

(3 citation statements)

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“…Dense collagen oriented vertically that may include stellate fibroblasts, variable dilated blood vessels 9 …”

Section: Discussionmentioning

confidence: 99%

Fetal‐hand‐like ungual fibrokeratoma

Godse

Jiang²,

Abbott

et al. 2023

J Cutan Pathol

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“…Dense collagen oriented vertically that may include stellate fibroblasts, variable dilated blood vessels 9 …”

Section: Discussionmentioning

confidence: 99%

Fetal‐hand‐like ungual fibrokeratoma

Godse

Jiang²,

Abbott

et al. 2023

J Cutan Pathol

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“…Multiple Koenen tumors affecting all digits are uncommon [1, 5-8]. The size may vary from 1 mm to 1 cm, and they can sometimes form large masses affecting all the digits [6]. Large florid masses may become confluent and keratotic and are often misdiagnosed and mistreated as fibrokeratomas or periungual warts [1, 5].…”

Section: Discussionmentioning

confidence: 99%

Multiple Koenen Tumors, a Rare Entity: Combination Treatment with 1% Topical Sirolimus Electrofulguration and Excision

Viswanath

Gupte²,

Prabhu³

et al. 2020

Skin Appendage Disord

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Introduction: Koenen tumors are benign, cutaneous manifestations of tuberous sclerosis. These are disfiguring, painful, and challenging to treat as they frequently recur. We report a case of long-standing, multiple Koenen tumors affecting all twenty nails in an elderly female who was successfully treated with a combination of topical sirolimus 1%, surgical excision, and electrofulguration. Case Report: A 57-year-old lady presented with multiple, asymptomatic periungual, and subungual tumors affecting all twenty nails since 27 years. Cutaneous examination revealed confetti macules, ash-leaf macule, and shagreen patch over trunk. Nail biopsy was compatible with Koenen’s tumor. Computerized tomography of brain showed diffuse patchy sclerosis. The tumors were treated with topical sirolimus 1% ointment for 10 months with excellent regression. Electrofulguration for both great toenails and surgical excision of right thumbnail periungual fibroma was done. 1% sirolimus was advised after the surgical treatment. There were no adverse effects or recurrence of tumors over a 2-year follow-up. Discussion: Topical sirolimus 1% was effective in tumor regression and preventing new tumor formation. Larger tumors that interfered in daily chores were treated with excision and electrofulguration. Thus, a combination treatment for this rare presentation of tuberous sclerosis provided optimum results.

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“…Other cutaneous manifestations include ash leaf macule, shagreen patch, and periungual fibroma Figure 6. [31]…”

Section: Introductionmentioning

confidence: 99%