Myopericytoma of the Maxillofacial Region: A Report of Two Cases

Abstract

Myopericytoma (MPC) was accepted as a separate entity by the World Health Organization in 2002 and it describes a lesion which comprises of myoid-like oval to spindle-shaped cells with a concentric perivascular type of growth. We present two unusual cases of MPC in the maxillofacial region. In our case management included complete surgical excision under general anesthesia and regular post-operative follow up. Myopericytomas belong to one of the three categories comprising a broader and heterogeneous group of lesions called Hemangiopericytoma (HPC)-like neoplasm's. These include glomangiopericytoma, infantile myofibromatosis (formerly known as infantile HPC), and portion of sinonasal HPC. A clinically relevant characteristic of hemangiopericytoma is its unpredictable clinical course which is often not related to its histopathologic characteristics. The latter course is in contrast to the benign course of MPC, thus it is essential for practitioners to differentiate between those two diagnoses.