Neonatal Presentation of Congenital Portosystemic Shunt

Congenital intrahepatic portosystemic shunt with spontaneous resolution in a newborn with severe fetal growth restriction

“…However, few neonatal cases of IPSS detected by abdominal ultrasonography screening at birth have been reported 2 . Some small IPSSs resolve spontaneously by 1–2 years of age, whereas others, mostly large shunts, remain into adulthood and require surgical and endovascular treatments 2,8 . Table 1 shows the summary of newborns with IPSS from the previous retrospective cohort studies, including the data on prenatal diagnosis and spontaneous closure 4,9–12 .…”

“…2 Some small IPSSs resolve spontaneously by 1-2 years of age, whereas others, mostly large shunts, remain into adulthood and require surgical and endovascular treatments. 2,8 Table 1 shows the summary of newborns with IPSS from the previous retrospective cohort studies, including the data on prenatal diagnosis and spontaneous closure. 4,[9][10][11][12] In mild cases, early detection may not be needed due to spontaneous closure, but in severe or persisting cases, early detection by ultrasonography could enable sufficient time for patients, families, and physicians to prepare for the treatment.…”