Nevus Lipomatosis Cutaneous Superficialis – A clinicopathologic study of the solitary type

Abstract

m e d i c a l j o u r n a l a r m e d f o r c e s i n d i a 7 2 ( 2 0 1 6 ) 6 7 -7 0 a r t i c l e i n f o Results: Mean age of the patients was 42.5 years. These lesions were more common in adult females (5/7). Thigh was the commonest location (4/7). The mean duration of these lesions was 2.0 years. Clinical diagnosis was papilloma (4/7) and acrochordon (3/7). Histopathology revealed the presence of varying amounts of mature ectopic adipocytes in the dermis located around dilated, ectactic blood vessels. Disorganised dermal collagen bundles and atrophic pilosebaceous units were seen.Conclusion: This study is a first from the Indian subcontinent and highlights the need for awareness of this rare clinical condition both by the dermatologists and the surgeons.Histopathology is essential for diagnosis as clinically they may mimic papillomas or skintags. An early diagnosis may permit a more conservative resection of the tumour. #

Topical corticosteroid therapy: a treatment option for nevus lipomatosus cutaneous superficialis?

“…Surgical excision is an appropriate option if the patient decides to treat. 1 , 4 We report an unusual case of classic NLCS, with onset in an atypical age group that had satisfactory clinical response with topical corticosteroid treatment.…”

“…The nevus lipomatosus cutaneous superficialis (NLCS) is a rare benign hamartomatous tumor. 1 - 3 It presents in two clinical forms: the classic and the solitary. The classic form usually occurs in childhood and adolescence and is characterized by multiple asymptomatic, soft, cerebriform, pedunculated, yellow or skin-colored papules, nodules or plaques.…”

“… 3 The solitary form is uncommon and usually affects individuals older than 20 years of age; it presents as a single sessile papule or dome-shaped lesion. 1 …”

“…NLCS was first described by Hoffmann and Zurhelle in 1921. 1 It is a benign and idiopathic malformation, characterized by the presence of mature ectopic fat tissue among the collagen bundles in the dermis. 4 Familial occurrence was not seen, and neither was gender predilection or association with other systemic conditions.…”

“…There are two forms of NLCS: the classical form, described by Hoffmann and Zurhelle, and the soliand the solitary form, both with chronic and asymptomatic course. 1 , 4 In the classical form, multiple papules are seen, coalescing into plaques, with a zosteriform, linear or segmental distribution. They are skin colored or yellow, soft or with a cerebriform surface, and can reach large dimensions.…”