New Described Dermatological Disorders

Abstract

Many advances in dermatology have been made in recent years. In the present review article, newly described disorders from the last six years are presented in detail. We divided these reports into different sections, including syndromes, autoinflammatory diseases, tumors, and unclassified disease. Syndromes included are “circumferential skin creases Kunze type” and “unusual type of pachyonychia congenita or a new syndrome”; autoinflammatory diseases include “chronic atypical neutrophilic dermatosis with lipodystrophy and elevated temperature (CANDLE) syndrome,” “pyoderma gangrenosum, acne, and hidradenitis suppurativa (PASH) syndrome,” and “pyogenic arthritis, pyoderma gangrenosum, acne, and hidradenitis suppurativa (PAPASH) syndrome”; tumors include “acquired reactive digital fibroma,” “onychocytic matricoma and onychocytic carcinoma,” “infundibulocystic nail bed squamous cell carcinoma,” and “acral histiocytic nodules”; unclassified disorders include “saurian papulosis,” “symmetrical acrokeratoderma,” “confetti-like macular atrophy,” and “skin spicules,” “erythema papulosa semicircularis recidivans.”

Multifocal and refractory pyoderma gangrenosum: Possible role of cocaine abuse

“…In 50% of cases, PG is associated with an underlying disease such as inflammatory bowel disease, rheumatological disease, haematological disorders or recently, metabolic syndrome . It has also been described as part of the spectrum of autoinflammatory disorders (pyogenic arthritis, pyoderma gangrenosum, acne, and hidradenitis suppurativa syndromes) associated with mutations in MTHFR and JAK genes . Certain drugs (sulpiride and haematopoietic growth factors) can also trigger PG‐like eruptions.…”

PASH Syndrome: The First Case Report from Iran

“…PASH syndrome is one of the newly described dermatological disorders (10,11). It is stated in previous reports that the level of pro-inflammatory markers such as cytokines and interleukins increased in PASH syndrome (7).…”

An Atypical Figurate Erythema With Seasonal Recurrences

“…3 While the disease course of this disorder might share some similarities with annually recurring erythema annulare centrifugum, 4 for some authors its clinical presentation differs slightly enough to consider it an independent entity. 1,2 Differential diagnosis in figurate erythemas can be challenging. A good clinical history and clinicopathological correlation in this setting is of utmost importance.…”

“…Erythema papulosa semicircularis recidivans (EPSR) represents a novel cutaneous disorder that manifests as centrifugally spreading semicircular erythematous plaques that typically relapse every year during the warm seasons and resolve in autumn . First described by Song et al in 2012, their case series of 9 middle-aged Chinese men ages 24 to 39 years from the Chongqing or Sichuan provinces presented with similar large figurate erythemas in the trunk that recurred yearly every summer.…”