Nonketotic Hyperglycemic Chorea in a 10-Year-Old Asian Boy with Diabetes Mellitus

Abstract

Nonketotic hyperglycemic chorea-ballism (NKHCB), also known as diabetic striato-pathy (DS) by some, is a rare complication of diabetes mellitus and uncommon in children. We report a case of a 10 11/12-year-old boy of Asian descent with uncontrolled type 1 diabetes mellitus (T1DM), Hashimoto's thyroiditis, and multiple food allergies presenting with bilateral chorea-ballism. His brain magnetic resonance imaging revealed developmental venous anomaly in right parietal lobe and right cerebellum, no focal lesions or abnormal enhancements. Choreiform movements resolved with correction of hyperglycemia. Children and adolescents with a movement disorder should be evaluated for diabetes mellitus, especially with increasing prevalence and insidious nature of T2DM associated with obesity.

Glycaemic Imbalances in Seizures and Epilepsy of Paediatric Age: A Literature Review

“…Chronic epilepsy may residue in some cases [ 123 , 124 ]. Like adults, children may also exhibit hemichorea/hemiballismus, in most cases mutually exclusive with seizures [ 125 , 126 ]. The outcome of seizures in children with HHS is usually favourable when an expedite metabolic treatment is established and brain lesions are prevented, even though there are exceptions.…”