Nutritional Rehabilitation in Neuromuscular Disorders

Willig, T.N.; Bach, John R.; Venance, Varille; Navarro, J.

doi:10.1055/s-2008-1041002

Cited by 30 publications

(19 citation statements)

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“…The monitoring and triggers for referral to an expert dietitian/nutritionist in DMD are described in panel 2. [128][129][130][131][132] Diet should be assessed for energy, protein, fluid, calcium, vitamin D, and other nutrients. We recommend that each patient should receive a daily multivitamin supplement with vitamin D and minerals.…”

Section: Nutritional Managementmentioning

confidence: 99%

Diagnosis and management of Duchenne muscular dystrophy, part 1: diagnosis, and pharmacological and psychosocial management

Bushby

Finkel

Birnkrant

et al. 2010

The Lancet Neurology

1,721

1,596

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Section: Nutritional Managementmentioning

confidence: 99%

Diagnosis and management of Duchenne muscular dystrophy, part 1: diagnosis, and pharmacological and psychosocial management

Bushby

Finkel

Birnkrant

et al. 2010

The Lancet Neurology

1,721

1,596

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“…Secondly, certain intercurrent events, such as infections, are known to increase muscle catabolism [10]. However, overfeeding to improve muscle protein synthesis [11] is ineffective [12] and can cause obesity in children with DMD [13]. In severely affected patients, still breathing spontaneously, it carries the risk of acute hypercapnia due to an increased carbon dioxide production that cannot be matched by a corresponding increase in alveolar ventilation [14,15] unless MV is provided.…”

mentioning

confidence: 99%

Resting energy expenditure in Duchenne patients using home mechanical ventilation

Gonzalez-Bermejo

Lofaso²,

Falaize³

et al. 2005

Eur Respir J

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Nutritional status is both important and difficult to assess in patients with Duchenne muscular dystrophy (DMD), particularly in those requiring mechanical ventilation (MV). The current authors evaluated body composition (bio-impedancemetry), resting energy expenditure (REE; indirect calorimetry) and energy intake in 20 adult patients with DMD using home MV (nocturnal: n513; continuous: n57) and 12 age-matched healthy controls.The patients were smaller in height than the controls and had a lower body weight. Most of the reduction in body mass index was accounted for by a reduction in fat free mass (FFM). REE (kJ) was significantly reduced in the patients (4559¡853 kJ?24 h -1 versus 7407¡1312 kJ?24 h -1), but the difference disappeared after correction for FFM.REE and FFM were correlated in both the controls and patients, but less strongly in the latter, the lower strength of the association being due to the patients using continuous MV (REE and FFM uncorrelated). The food intake of the patients was 1.2¡0.4 greater than their REE.This study shows that patients with advanced forms of Duchenne muscular dystrophy have balanced energy intakes and resting energy expenditure.

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“…Quality of life, however, declines over time as the disease progresses. Malnutrition is common: in one study, for instance, 44% of patients had malnutrition (Willig, Bach et al 1995;Finder, Birnkrant et al 2004). The main causes of malnutrition are prolonged swallowing, respiratory failure, and dysphagia, which jeopardize the patient's ability to meet intake needs.…”

Section: Breathing-swallowing Interaction In Neuromuscular Patientsmentioning

confidence: 98%

Noninvasive Monitoring of Breathing and Swallowing Interaction

Terzi¹,

David²,

Prigent³

et al. 2012

EMG Methods for Evaluating Muscle and Nerve Function

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Nutritional Rehabilitation in Neuromuscular Disorders

Cited by 30 publications

References 0 publications

Diagnosis and management of Duchenne muscular dystrophy, part 1: diagnosis, and pharmacological and psychosocial management

Diagnosis and management of Duchenne muscular dystrophy, part 1: diagnosis, and pharmacological and psychosocial management

Resting energy expenditure in Duchenne patients using home mechanical ventilation

Noninvasive Monitoring of Breathing and Swallowing Interaction

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