Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome: A case report

Abstract

Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome is a rare congenital abnormality marked by a triad of uterine didelphys, obstructed hemivagina, and ipsilateral renal anomaly. The condition is asymptomatic in the pre-pubertal females. Commonly it is diagnosed in young females, within a year of menarche, who present with cyclical pelvic pain with or without a mass. Rarely, these patients are identified later in life, many years after initiation of menses, and a high clinical index of suspicion must be kept. Presented here is a case of OHVIRA syndrome diagnosed in a 22-year-old nulliparous female who presented to the Accident and Emergency Department (AED) of the Queen Elizabeth Hospital, Barbados, with a two-month history of abdominal pain. A laparotomy with right ovarian cystectomy and vaginal incision and drainage of left hematocolpos with marsupialization was performed and the patient was discharged with no complications.