Occipital encephalocele associated with Dandy-Walker malformation: a case-based review

Pineda, Felipe Gutierrez; Ballestero, Matheus Fernando Manzolli; Herrera, David; González, Catalina; Cardona, Alejandra; Mora, Laura

doi:10.1007/s00381-022-05551-2

Cited by 3 publications

(5 citation statements)

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“…However, the research is consistent as far as mental and motor abilities are concerned. [15][16][17] It has been determined that the prognosis of the patient is impacted by how much neural tissue there is inside the abnormality, as well as any concomitant congenital defects or infections that may be present, presence of vascular structure, size of encephalocele compared to the size of the skull. 14,15.…”

Section: Discussionmentioning

confidence: 99%

“…According to a study by Rehman et al, 13 before encephalocele repair can be completed, a VP shunt must be installed. Kabré et al, 7 suggested that when preoperative hydrocephalus is present, encephalocele should be addressed as well. Surgical wounds from encephaloceles should be treated with antibiotics only after the hydrocephalus has healed to reduce the risk of infection.…”

Section: Discussionmentioning

confidence: 99%

“…Medical literature does not readily report shunt dysfunction rates in encephalocele series. 7,13,14 DaSilva et al, 9 published that in 3.7 years of follow-up, found a malfunction rate of 20%. 90% of shunt dysfunction events occurred in the first 24 months of follow-up in our cohort, which had an 8% shunt dysfunction rate, as seen by the Kaplan-Meier survival curve that was shown.…”

Section: Discussionmentioning

confidence: 99%

“…Though most series are based on real-life events. 7,9,13,14 VP shunts are the most common treatment for hydrocephalus, although ETV may be an option when the patient's age and anatomy are appropriate. This study has several drawbacks, including a retrospective nature, a limited sample size, and no follow-up data.…”

Section: Discussionmentioning

confidence: 99%

“…The primary theory of its etiology proposes that a deficiency in the dura and the calvaria, which might allow the cerebral material to protrude through, results from an aberration in mesodermal development, [4][5] Even though some researchers have hypothesized a link between encephaloceles and spina bifida and anencephaly. [6][7] There is a wide range of encephalocele incidence, ranging from 0.8 to 5.6 per 10,000 live births. 8 Despite the disease's rarity, it is still in high demand in developing and emerging countries, such as Brazil, where abortion is only permitted in extremely rare circumstances.…”

Section: Introductionmentioning

confidence: 99%

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Association of Hydrocephalus in Children with an Encephalocele

Habib,

Bokhari,

Ahmed

et al. 2023

Pak J Neurol Surg

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Objectives: To describe the association between the occipital encephaloceles with hydrocephalus and how to improve the outcome of patient. Methodology: Our Prospective study collected records of fifty patients diagnosed with posterior encephaloceles. Data were collected on the gender, location of the encephalocele, presence of neural tissue , dandy walker, microcephaly and hydrocephalus. Results: Twenty-nine females and twenty-one males were present. Over half of the lesions were supratorcular, while the remaining eight (16%) were torcular and the remaining seventeen (34%) were infratorcular. Primary encephalocele repair were done at an average of 9 days (range 2.5–120 days). In twenty-five of the instances, a diagnosis of hydrocephalus was made. Twenty-four patients had a ventriculo-peritoneal shunt implanted. The average age of implantation of VP shunt was only 1.2 months (range 0.3–9 months). One patient underwent an endoscopic third ventriculostomy with good results. Hydrocephalus was related with Dandy-Walker and ventriculomegaly before encephalocele surgery was performed (p values 0.01 and 0.05, respectively). For hydrocephalus therapy, Conclusions: Patients born with encephaloceles frequently suffer from hydrocephalus (50%). This is especially true in cases where the patient also has Dandy-Walker syndrome, CMIII malformation, or pre-existing ventriculomegaly. The severity of large encephaloceles is a limiting factor for the development of hydrocephalus when connected with torcular types and microcephaly.

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Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%