OHVIRA syndrome in an infant girl

Sahab, Ruba; El-Desoky, Sherif M.; Al-Sayyad, Ahmed; Kurdi, Mazen O.; Kari, Jameela A.

doi:10.4103/ajpn.ajpn_16_19

Cited by 1 publication

(2 citation statements)

References 16 publications

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“…However, all of these classifications are not correlated with their associated anomalies. In the uncommon case of OHVIRA, there can also be unusual periods, such as in the newborn, prepubertal period, or presenting with multiple variants [3,4,13]. A review of 734 cases showed dysplastic or multicystic kidney (7.8%), endometriosis (13.6%), a single uterus (0.4%) or in other case reports, an ectopic ureter or a duplicated ureter [14][15][16] .…”

Section: Discussionmentioning

confidence: 99%

“…There are various anomalies even though the presenting symptoms are in the same pattern. Interestingly, uncommon cases can present with the symptoms shortly after birth (within the first 6 months after delivery) due to withdrawal of maternal estrogen hormone and causing vaginal bleeding [3,4]. The rare variants of the classical syndrome were average of 27.6% such as uterus septum, ectopic ureter [5].…”

Section: Introductionmentioning

confidence: 99%

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Optional Method with Innovative Instrument for Ohvira Syndrome Treatment: Case Reports and Review of Literature

Satirapod¹

2023

J Gynecol Res Rev Rep

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OHVIRA syndrome is a rare condition usually present during early puberty, after menarche. The main symptoms are caused by the obstruction of hemivagina and accumulation of blood, which cause the symptoms such as dysmenorrhea, chronic pelvic pain or pelvic mass. Transvaginal septectomy is the best way to treat of patient’s obstructive hemivagina. However, in young patients, the small vagina canal is a significant limitation, and it is challenging to explore the surgical field. Due to the uncommon condition at young ages and variation in coexisting anomalies, approach techniques and instruments are still under development. In this case series, we present 2 cases of OHVIRA syndrome who received surgical treatment at Ramathibodi Hospital, Mahidol University. Both cases used the same innovative vaginal retractor, designed and modified for the young patient with OHVIRA syndrome. After the procedure, patients showed no complications or recurrence up to 2 years of follow-up.

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