Ophthalmic Sequelae of Crouzon Syndrome

Gray, Timothy L.; Casey, Theresa; Selva, Dinesh; Anderson, Peter J.; David, David J.

doi:10.1016/j.ophtha.2004.12.037

Cited by 85 publications

(68 citation statements)

References 28 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…This indicates towards the importance of ophthalmic examination in newborns with craniofacial anomalies as early as possible, even before corrective surgeries. In a retrospective study on patients with Crouzon's syndrome by Silva et al, 9 visual impairment was found in at least 1 eye in 35% of patients and was bilateral in 9% of patients. The most common cause of visual impairment was amblyopia, which was present in 21% of patients, followed by optic atrophy in 7%.…”

Section: Resultsmentioning

confidence: 93%

“…Dysmorphism affecting size or shape of the globe 15 explains the reason for higher incidence of refractive errors in patients with craniofacial anomalies compared to general population. In a study 9 with a sample size of 131 patients with Crouzon Syndrome by Silva et al, 35% of the patients were found to have a visual impairment in at least one eye. In a similar study on Apert syndrome by Khong et al, 16 54% of the 61 patients were found to have visual impairment in at least one eye.…”

Section: Resultsmentioning

confidence: 98%

“…8 In our study, 34 patients had Crouzon's syndrome. Crouzon's syndrome 8,6,9 is characterised by acrocephaly, exophthalmos, hypertelorism, strabismus, parrot-beaked nose, and hypoplastic maxilla. All patients in our study who were diagnosed to have Crouzon's syndrome had ocular involvement.…”

Section: Resultsmentioning

confidence: 99%

“…In our study, we found out that 18% of the patients were amblyopic. Studies have shown an incidence of amblyopia 9,17 between ranges of 20% to 35 % of all patients. This clearly indicates towards the importance of ophthalmic examination as early as possible in patients with craniofacial anomalies in order to prevent permanent damage of eye.…”

Section: Resultsmentioning

confidence: 99%

See 3 more Smart Citations

Ocular Manifestation in Patients With Craniofacial Anomalies - A Hospital Based Study

M¹,

Shetty²,

Pai³

2016

jemds

View full text Add to dashboard Cite

BACKGROUND Ocular manifestations in Children with Craniofacial Anomalies are an important but easily overlooked part as the patient and his family tends to be more focused on the more visible cosmetic disfigurement. The disfigurement while may be corrected in the hands of a competent surgeon at a later date, more lasting harm may be done to the patient's well-being if simple correctable refractive or other ocular conditions are left too late. This study was done to detect ocular involvement in patients with craniofacial anomalies and also to emphasise importance of routine ophthalmic examination in these patients. MATERIALS AND METHODSThis was a cross-sectional observational type of study. Study duration was dated from dated from November 2012 to October 2014. All patients who presented to the Department of Ophthalmology of Justice KS Hegde Medical College Hospital, Mangalore with craniofacial anomalies were included in this study. All patients with CFA were included in the study irrespective of age of presentation, gender or history of previous corrective surgery. The patients were evaluated at the time of presenting to the Department of Ophthalmology of Justice KS Hegde Medical College, Mangalore. Duration of this study was dated from November 2012 to October 2014. RESULTSOut of the 151 patients screened, 47.68 % (n=72) of the patients had one or the other forms of ocular anomalies. Patients with craniosynostosis had 100% ocular involvement (n=39). In patients with clefting syndrome, 29.46% of the patients had ocular involvement (n=33). Refractive error was most common ocular anomaly detected in our study. 49.01% of the patients in our study had refractive error out of which 22.51% of the patients were hypermetropes. CONCLUSIONFindings in our study suggest that there are numerous ocular associations in patients with craniofacial anomalies. A routine ophthalmic evaluation would help in early diagnosis of these ocular conditions and early management which would greatly benefit the patient.

show abstract

Section: Resultsmentioning

confidence: 93%

Section: Resultsmentioning

confidence: 98%

Section: Resultsmentioning

confidence: 99%

Section: Resultsmentioning

confidence: 99%

See 2 more Smart Citations

Ocular Manifestation in Patients With Craniofacial Anomalies - A Hospital Based Study

M¹,

Shetty²,

Pai³

2016

jemds

View full text Add to dashboard Cite

show abstract

“…[4][5][6] Surgical management is indicated for two reasons. Growth restriction in the presence of a rapidly expanding growing brain may result in raised ICP, 7 and surgery may be indicated for the prevention or treatment of raised ICP.…”

Section: Nonsyndromic Craniosynostosesmentioning

confidence: 99%

Craniofacial surgery for orbital malformations

Richardson

Thiruchelvam

2006

Eye

View full text Add to dashboard Cite

Paediatric craniofacial surgery is a highly specialised field requiring a multidisciplinary team input. Orbital and ocular involvement is relatively common in craniofacial patients. This is more in syndromic patients. In nonsyndromic patients, orbital involvement is common in frontal plagiocephaly and trigonocephaly. The management of these conditions requires close working between the craniofacial surgeon and ophthalmologist. An outline of the management of these deformities is discussed.

show abstract

Craniofacial Synostoses

Rowe¹

2012

Clinical Orthoptics

View full text Add to dashboard Cite

Ophthalmic Sequelae of Crouzon Syndrome

Cited by 85 publications

References 28 publications

Ocular Manifestation in Patients With Craniofacial Anomalies - A Hospital Based Study

Ocular Manifestation in Patients With Craniofacial Anomalies - A Hospital Based Study

Craniofacial surgery for orbital malformations

Craniofacial Synostoses

Contact Info

Product

Resources

About