Optimizing outcomes and bridging biliary atresia into adulthood†‡

Sokol, Ronald J.; Mack, Cara L.

doi:10.1002/hep.20575

Cited by 16 publications

(10 citation statements)

References 22 publications

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“…Our data show that, consistent with previous studies, 12,13,16,25,35,36,40,42,43 those who had a delayed PE (after 60 days old) had a worse 5‐year native liver survival rate. We also found the percentage of cases receiving LT during 1999–2003 was higher than that during 1996–1998 and this was accompanied with a better 5‐year overall survival rate.…”

Section: Discussionsupporting

confidence: 91%

Epidemiological features of biliary atresia in Taiwan, a national study 1996–2003

Tiao¹,

Tsai²,

Kuo³

et al. 2007

J of Gastro and Hepatol

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Section: Discussionsupporting

confidence: 91%

Epidemiological features of biliary atresia in Taiwan, a national study 1996–2003

Tiao¹,

Tsai²,

Kuo³

et al. 2007

J of Gastro and Hepatol

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“…These include the center effect (i.e. the experience of the center involved in performing the Kasai), differences in postoperative medical care, and perhaps genetic differences [68].…”

Section: Managementmentioning

confidence: 99%

Closing in on Biliary Atresia

Hardikar¹,

Schwarz

2006

CPR

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Biliary atresia (BA) is a rare congenital condition which results in significant morbidity and mortality. The Kasai hepatic portoenterostomy and liver transplantation have significantly improved survival in this disease; however, unraveling the etiology/etiologies will be required to improve transplantation free survival. At present, BA is still the single most common condition in children on pediatric liver transplant waiting lists and accounts for up to 50% of those waiting for liver transplantation [1]. It is the most rapidly fibrosing liver disease in man and accounts for ~10% of all liver transplant procedures performed [2]. The rarity of this condition and the likelihood of a multi-factorial etiology have limited progress in research. Recently, collaborative research networks in North America (BARC) and Europe (EBAR) have been established [3,4]. The following discussion outlines the most recent information available from these and other groups concerning epidemiology, pathophysiology, etiology, diagnosis, management, long term outcome and conclusions/ recommendations for future research.

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“…However, nearly all BA patients suffer from a chronic liver disease and the liver-transplanted patients are always threatened by organ rejection, for the rest of their lives [61].…”

Section: Outcomementioning

confidence: 99%

Biliary atresia: interdisciplinary initiatives focus on a rare disease

Petersen

2007

Pediatr Surg Int

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During the last decade, biliary atresia (BA) has attained more interest and the frequency of BA-related publications has increased continuously. Pediatric hepatologists and pediatric surgeons are very active in improving diagnosis and treatment modalities of BA patients, in order to prolong the survival rate of their native liver. Together with transplant surgeons, the bridging of BA patients to liver transplantation (LTx) becomes optimized and as a consequence of this interdisciplinary approach, the overall survival of babies with BA has already reached 90%. Furthermore, basic research into the still unknown origin of BA has advanced, and numerous scientific programs have already linked together. The overriding interest is to discover at least BA's etiology and to turn the treatment of BA patients from a symptomatic to a causative approach. Interdisciplinary and international programs are mandatory and already existing initiatives in Europe, the United States and Japan are going to coordinate their registries, clinical trials and basic research studies for the benefit of the patients and solve the riddle of BA.

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Optimizing outcomes and bridging biliary atresia into adulthood†‡

Cited by 16 publications

References 22 publications

Epidemiological features of biliary atresia in Taiwan, a national study 1996–2003

Epidemiological features of biliary atresia in Taiwan, a national study 1996–2003

Closing in on Biliary Atresia

Biliary atresia: interdisciplinary initiatives focus on a rare disease

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