Background: An oropharyngeal tumor presenting as a protruding mass from the mouth of the newborn infant is very rare. This mass has the potential to obstruct the airway and requires urgent medical management, diagnosis and appropriate surgical management. Objectives: To report a case of a newborn with an oropharyngeal mass presenting at birth and focus on key clinical issues for the physician faced with the care of such an infant. Methods and Results: We describe a newborn infant who was born with a large mass protruding from the oral cavity at birth, without respiratory distress. The mass was surgically removed with no complications. The histology of the mass revealed it to be a pharyngeal dermoid polyp, also called ‘hairy polyp’. The infant did well after tumor removal and was discharged home within a couple of days. Conclusions: We report a case of a newborn with a pharyngeal dermoid polyp presenting as an oropharyngeal mass.