Orbital haemangiopericytoma simulating an intraocular mass

An intraocular solitary fibrous tumor/hemangiopericytoma with extrascleral extension: Case report and review of literature

“… 3 , 5 , 6 , 7 , 8 , 9 Orbital SFT/HPC are less rare, although they are still found in less than 1% of all orbital biopsies. 10 , 11 No data exists on the epidemiology of intraocular SFT/HPC beyond the aforementioned case reports. All six cases originated from the uvea, with four of choroidal origin, 3 , 7 , 8 , 9 one of ciliary origin 6 and one supraciliary.…”

“…All six cases originated from the uvea, with four of choroidal origin, 3 , 7 , 8 , 9 one of ciliary origin 6 and one supraciliary. 5 Interestingly, a case report by Diniz et al 11 reported a SFT/HPC arising in the orbit behind the globe causing compression of the globe and mimicking an intraocular tumor. No race, ethnicity or gender predilection is known for SFT/HPC.…”

“…Including our case report, 4 cases of intraocular SFT/HPC have been reported in men and three in women. Although the tumor usually presents in patients aged 20–70 years, 11 the supraciliary SFT/HPC was reported in a ten-year-old child. 5 …”

“… 3 , 10 Extraocular orbital SFT/HPC typically arises as a painless, unilateral tumor within the muscle cone. 11 , 12 Patients may present with painless proptosis, visual disturbances, ocular motility restriction, a palpable mass, or blepharoptosis. 11 , 12 The presentation of intraocular SFT/HPC ranges broadly, including serous retinal detachments, 7 , 8 blurred vision, 6 , 9 intermittent eye pain, 5 and in one case was an incidental finding on a routine eye exam.…”

Treatment of orbital haemangiopericytoma with surgery and preoperative embolization

“…1,2 Incomplete resection is associated with a high rate of recurrence and malignant conversion. 2 Complete removal of the lesion is considered the mainstay treatment. 3 Gear et al 4 recommend radiotherapy for recurrent superficial tumour, however, radiotherapy carries the risk of ischaemic optic neuropathy, as does embolization.…”