Orbital Lymphangioma-Case Report and Review of the literature

doi:10.20431/2455-572x.0302003

Cited by 1 publication

(4 citation statements)

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“…With incomplete excision, the recurrence rate is very high, and patients may experience a prolonged and recurrent course [6,27]. Accordingly, surgical excision is not recommended as the first line of treatment.…”

Section: Discussionmentioning

confidence: 99%

“…Agents for orbital lymphangioma include OK-432, sodium tetradecyl sulfate (multiple manufacturers), 5% sodium morrhuate, and bleomycin A5 [25]. Sclerotherapy is an established management option for these lesions as a new line of treatment to reduce recurrence rate or in unresectable cases with good results in appropriately selected patients [6,25]. For patients with eyelid or orbital lymphangioma, injection of a sclerosant is a useful treatment, especially if no surgery is preceded on the patient [24], but there is always the risk of optic nerve damage [7].…”

Section: Discussionmentioning

confidence: 99%

“…Bleomycin has a sclerosing effect on endothelial cells and has been used to treat pleural effusion plus vascular anomalies [2]. Its side effects are erythema, edema, pain, local necrosis, and flagellate hyperpigmentation, which can be resolved with drug interruption [6]. Literature search exhibited a few reports about bleomycin injection for the treatment of lymphangioma without systemic or ophthalmic complications [33,34].…”

Section: Discussionmentioning

confidence: 99%

“…However, symptoms can appear slowly as a mass invading the orbit or suddenly during hemorrhage of the O lesion, leading to painful proptosis, compressive optic neuropathy, exposure keratopathy, increased intraocular pressure, restrictive ocular motility, and visual acuity changes [2,5]. These symptoms may appear after an upper respiratory infection or a minor trauma [6].…”

Section: Introductionmentioning

confidence: 99%

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Orbital Lymphangioma: A Case Report and Review of Management Modalities

Jafari

2021

J Pediatr Rev

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Background: Generally presents in childhood, orbital lymphangioma is an uncommon unencapsulated vascular malformation of the lymphatic system. These benign cystic lesions represent 1%-4% of all orbital masses and may appear after an upper respiratory infection or minor trauma. Because of its nature, the management can be challenging and depends on the clinical presentation. We report an 8-year-old boy with orbital lymphangioma presented with acute proptosis. Then, we discuss different features of this disorder plus its management Case Presentation: An 8-year-old boy was presented with sudden left eye proptosis. He had normal visual acuity and color vision without ocular pain or diplopia. An infiltrative and diffused intraconal plus extraconal mass was detected in orbital computed tomography. Contrast-enhanced MRI revealed a multilobulated infiltrative heterogeneous lesion with fluid-fluid levels. The diagnosis was made on imaging, and he went under treatment with an oral corticosteroid. The symptoms were entirely resolved, and no recurrence occurred during the follow-up. There are several surgical and nonsurgical therapies for orbital lymphangioma. Still, the priority is conservative management, such as sclerotherapy (including OK-432, doxycycline, sodium tetradecyl sulfate, etc.), bleomycin, carbon dioxide laser, systemic corticosteroids, and so on. Conclusions: In most cases, the current imaging methods make a noninvasive diagnosis of orbital lymphangioma possible. Conservative management should be considered the first treatment.

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Section: Discussionmentioning

confidence: 99%