Orbital Lymphangiomas: Surgical Treatment and Clinical Outcomes

Simas, Nuno; Farias, João Paulo

doi:10.1016/j.wneu.2013.01.098

Cited by 8 publications

(11 citation statements)

References 19 publications

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“…All the previous studies have reported excision of lymphatic lesions completely or partially followed by histological confirmation. Surgical attempts at excision often lead to partial resection, and reported recurrence rates have been variable, ranging from none to almost 71% 12 13…”

Section: Discussionmentioning

confidence: 99%

Management of a case of orbital lymphangioma presenting in adulthood with negative-pressure aspiration and bleomycin injection

Sen

Singh²,

Bajaj

et al. 2019

BMJ Case Rep

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We hereby report a case of a 55-year-old woman, with complaints of sudden onset outward protrusion of left eye progressing over 2 months, along with pain and loss of vision. Visual acuity in the affected eye was light perception only. On imaging, a well-defined solitary cystic lesion was noted in the retrobulbar space, which showed no enhancement on contrast-enhanced MRI. We performed fluid aspiration from the cyst under negative pressure and injected bleomycin as a sclerosant, without attempting a surgical excision. The proptosis reduced visibly, and after a week, visual acuity improved to finger counting at 1 m. At the 6 months follow-up, the patient did not show any recurrence of proptosis. This report highlights the importance of sclerosant therapy without the need for surgical excision in managing macrocystic lymphangiomas in adult age group.

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Section: Discussionmentioning

confidence: 99%

Management of a case of orbital lymphangioma presenting in adulthood with negative-pressure aspiration and bleomycin injection

Sen

Singh²,

Bajaj

et al. 2019

BMJ Case Rep

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“…[ 2 3 4 5 ] Lymphangiomas are common during the first decade of life. [ 6 ] Spontaneous hemorrhage occurs in 55% of the cases, resulting in sudden increase in size of tumor, loss of vision, proptosis, and compressive optic neuropathy. [ 2 3 7 ] Lymphangiomas are more common in males.…”

Section: Discussionmentioning

confidence: 99%

A case of intraorbital intraconal lymphangioma with post-traumatic apoplexy

et al. 2018

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Orbital lymphangioma is an infrequent benign cystic lesion manifesting in childhood and presenting with slowly progressive proptosis, and restriction of eye movements. Here we report a rare case of 8 year old male patient presenting with unilateral painful proptosis and subconjunctival hemorrhage with decrease of vision and restriction of eye movements. CT scan and MRI were done which revealed an intraorbital and intraconal cystic space occupying lesion. Fronto-orbito zygomatic craniotomy was done for orbital decompression and subtotal excision of tumor and blood evacuation. Histopathological findings were suggestive of lymphangioma.

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“…The patients may present with either slowly progressive symptoms, or sudden pain and tumor enlargement precipitated by an acute hemorrhage. 8 Wright et al 1 reported that the most prevalent manifestation in patients is mass effect (42%), followed by hemorrhage (37%), ocular motility changes (28%), and proptosis (15%). In advanced stages of the disease, the patients may also develop ophthalmoplegia and amaurosis.…”

Section: Discussionmentioning

confidence: 99%

“…This approach allows for an adequate exposure of the superior and lateral orbital walls and reduces the need for retraction and manipulation of the orbital contents. 8,12 Other treatment options are subtotal resection 14 , sclerosing agents, as OK-432 15 or sodium morrhuate, 16 as well as fractionated β-irradiation, but this may carry a unwanted risk of optic nerve damage. Moreover, percutaneous needle aspiration can be executed with a significant recurrence rate.…”

Section: Discussionmentioning

confidence: 99%

Orbital Lymphangioma: Case Report and Management Paradigms

et al. 2017

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Introduction Lymphangioma is a rare congenital vascular malformation of the head and neck region isolated from the systemic circulation. It has a benign etiology, and represents 1-3% of all orbital tumors. These hamartomas often present in the pediatric population with a slightly female predilection. They have a lymphocytic composition, and may increase in size with episodes of viral infection, causing proptosis. Discussion The management of this lesion is controversial, hardly curative, and depends on the clinical presentation. The treatment options include partial surgical resection of the major cyst, needle aspiration, surgical debulking, systemic steroids, sildenafil, intralesional injection of the sclerosing agents, and local radiotherapy. Case Report In the present report, we describe an uncommon case of lymphangioma in a 6-year-old female who was first submitted to neurosurgery for tumor resection and received sildenafil therapy later, with promising results. Conclusion The treatment of orbital lymphangiomas remains a controversial topic, and the use of sildenafil along with needle aspiration and microsurgical removal is a viable option of treatment. However, many issues, such as the ideal duration of the therapy, the dosage regimen and the recurrence rate, still remain unclear. Our case report adds promising data on this pathology, even though larger trials are needed to properly elucidate the remaining questions.

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Orbital Lymphangiomas: Surgical Treatment and Clinical Outcomes

Cited by 8 publications

References 19 publications

Management of a case of orbital lymphangioma presenting in adulthood with negative-pressure aspiration and bleomycin injection

Management of a case of orbital lymphangioma presenting in adulthood with negative-pressure aspiration and bleomycin injection

A case of intraorbital intraconal lymphangioma with post-traumatic apoplexy

Orbital Lymphangioma: Case Report and Management Paradigms

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