Oro-Dental Manifestations and Implications of the Osteolyses

Abstract

The Osteolyses are a group of uncommon genetic disorders which are characterized by progressive resorption of bone. This process ultimately results in significant physical handicap with pathological fractures representing an additional complication. The skeleton in the Osteolyses is radiolucent and the manifestations resemble those of Osteogenesis Imperfecta.A boy with a confirmed diagnosis of Torg-Winchester syndrome attended the metabolic bone clinic at Grey's Hospital and his clinical and radiological features have recently been published [1] . The dental and craniofacial manifestations of this boy form the subject of this article. These features tend to be overshadowed by the more dramatic skeletal changes in the limbs. Nevertheless, appropriate dental care is an important component of the overall management of this severe condition.