Outcome after Surgical Treatment of a Rare Congenital Pouch Colon Variant with Tubularized Coloplasty

Congenital Pouch Colon without Fistula: A Rare Variant

“…[3] CPC without fistula was seen in only 3 out of 68 cases in one study and 3 cases (all CPC type 1) in another study. [4,5] CPC without colovesical fistula is usually reported in type1 (25%) and type 2 CPC (75%), however, in the present case, it was encountered in type 4 CPC. [3] In conclusion, CPC without distal fistula should be considered an extremely rare variant of CPC.…”

“…CPC without fistula is rare and have been described only rarely. [2][3][4][5] In In a series of 32 cases of CPC in male babies, only 1 patient had CPC without a fistula vindicating its extreme rarity. [2] In a recent series of four case of CPC without fistula, Down's syndrome (1), cardiac lesion (2), pneumoperitoneum at time of presentation (2) and all were high type of ARM.…”