Pansclerotic morphea: a historical case in children

Abstract

Morphea is a variant of localized scleroderma in which lesions are usually limited to the skin and subcutaneous tissue. Pansclerotic morphea is a rare atrophying and sclerosing type of morphea. It can follow a comparatively benign course with spontaneous resolution of symptoms, or sometimes can lead to a variety of complications resulting in progressive disability. We report a case of pansclerotic morphea in an 4-year-old female child involving the right upper limb, resistant to treatment and the cause of a major functional and esthetic damage.