Papillon-lefevre syndrome: A combined approach from the dermatologist and dentist - A clinical presentation

Muppa, Radhika; Prameela, B; Duddu, Mahesh Kumar; Dandempally, Arthi

doi:10.4103/0019-5154.91843

Cited by 12 publications

(26 citation statements)

References 9 publications

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“…Oral rehabilitation of patients suffering from premature loss of teeth due to trauma, infection or a genetic disorder is quite challenging . ROD is associated with early loss of teeth subsequent to either intended teeth extractions or infection.…”

Section: Discussionmentioning

confidence: 99%

Oral rehabilitation of a case with regional odontodysplasia using a regenerative approach—A case report and a review of literature

Abdel‐Kader

Abdel-Azeem

Ahmed

et al. 2019

Special Care in Dentistry

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Aim to investigate for the first time whether the regenerative approach can be used to rehabilitate a case with regional odontodysplasia (ROD). ROD is a rare, localized developmental anomaly of the dental tissues. Moreover, we review the various treatment protocols for ROD and compare them to the suggested regenerative protocol. Case Report A 22‐year‐old female patient diagnosed with ROD in the upper left quadrant was presented to our clinic. Initially, the affected teeth were extracted and three implants were inserted. A combination of autologous bone marrow mononuclear cells (BMMNCs) seeded on a collagen sponge, nanohydroxyapatite, and autologous platelet‐rich fibrin (PRF) was used to enhance bone regeneration in the defective area and around the inserted implants. After 9 months, bone regeneration and successful osteointegration around the inserted implants were achieved, permitting the insertion of a fourth implant. After an additional six months, a final fixed restoration was constructed. Conclusion The suggested regenerative approach provides a better treatment option for ROD patients to regenerate the lost bone, rehabilitate aesthetics, and restore normal function.

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Section: Discussionmentioning

confidence: 99%

Oral rehabilitation of a case with regional odontodysplasia using a regenerative approach—A case report and a review of literature

Abdel‐Kader

Abdel-Azeem

Ahmed

et al. 2019

Special Care in Dentistry

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“…Conditions with such similar appearance are seen in malignancies, severe periodontal disease, papillon-lefevre syndrome etc., [8].…”

Section: Discussionmentioning

confidence: 99%

Multifocal Eosinophilic Granuloma of Jaws and Skull with Classical and Unusual Radiographic/Imaging Findings

Raviraj¹

2017

JCDR

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A 37-year-old male patient reported with a chief complaint of loosening of teeth in lower front teeth region since three years. Patient gave a history of trauma to the left skull and left mandibular body region five years back in a road traffic accident. Following the trauma patient did not observe any changes related to his medical and dental health. Patient underwent extraction of teeth no #36,37 due to mobility four months back. The rest of the missing teeth i.e., teeth no #25,26,35,43,45,46 got exfoliated a year back. Patient's past medical history was non-contributory. Extraoral examination revealed no abnormality. Intraoral examination revealed flattening of mandibular left and right posterior alveolar ridges with unhealed sockets in mandibular left posterior region. The gingiva and other mucosal areas did not exhibit any abnormalities. The mucosa covering the residual ridges of mandible appeared as if it was ulcerated due to unhealed sockets in the missing teeth in mandibular left posterior region [Table/ Fig-1a]. On palpating the lingual aspect of mandibular left posterior region a bony hard swelling was appreciable, which corresponded to the periosteal reaction in the occlusal radiograph. The residual ridge of mandibular right posterior region appeared to be flattened. However, the mucosa covering the same appeared normal [ Table/ Eosinophilic granuloma is basically a disorder of reticuloendothelial system and is one of the variants of langerhans cell histiocytosis. Multifocal eosinophilic granuloma affecting jaws and skull is relatively a rare disorder. We hereby report a case of multifocal eosinophilic granuloma involving mandible, maxilla and several skull bones. The present case has mixture of classical floating teeth appearance and an unusual radiographic/imaging finding of periosteal remodeling, which is rarely seen in adult patients of eosinophilic granuloma and pseudo-multilocular appearance in anterior mandibular region in coronal sections and moth-eaten appearance of skull was appreciated in axial slices of Computed Tomography (CT).[

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“…[1] It is transmitted as an autosomal-recessive inheritance. Consanguinity of parents is evident in about one third of cases.…”

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confidence: 99%

“…Consanguinity of parents is evident in about one third of cases. [1] It was first described by two French physicians, Papillon and Lefevre, in 1924. [2] It has a prevalence of 1-4 cases per million persons.…”

mentioning

confidence: 99%

“…[3] Majority of the teeth are lost by the age of 14-15 years. [1] The teeth erupt normally but are soon lost. [45] In addition to palmoplantar keratosis and periodontitis, other clinical findings in this condition include recurrent pyogenic skin infections, acro-osteolysis, atrophic changes of the nails, arachnodactly, and a peculiar radiographic deformity of the finger consisting of tapered, pointed phalangeal ends, claw like volar curve, and pes planus.…”

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confidence: 99%

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Papillon-Lefevre syndrome: Two siblings, one developing liver abscess

et al. 2013

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Papillon-lefevre syndrome: A combined approach from the dermatologist and dentist - A clinical presentation

Cited by 12 publications

References 9 publications

Oral rehabilitation of a case with regional odontodysplasia using a regenerative approach—A case report and a review of literature

Oral rehabilitation of a case with regional odontodysplasia using a regenerative approach—A case report and a review of literature

Multifocal Eosinophilic Granuloma of Jaws and Skull with Classical and Unusual Radiographic/Imaging Findings

Papillon-Lefevre syndrome: Two siblings, one developing liver abscess

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