Paraesophageal mediastinal desmoid tumor: case report

Nakagiri, Tomoyuki; Koseki, Masato; Nakamoto, Kenbu; Taniyama, Kiyomi

doi:10.1007/s11748-006-0068-4

Cited by 8 publications

(3 citation statements)

References 10 publications

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“…Aggressive fibromatosis is a locally invasive (myo)fibroblastic proliferation with bland cytology and without metastatic potential. About 30 cases of primary mediastinal aggressive fibromatosis (AF) have been reported as case reports, many of which were included in reviews by Nakagiri et al and Bouchikh et al [ 113 , 114 ] AF in the mediastinum occurs mainly in younger individuals (age range 3–67 years; median 38 years) [ 113 – 119 ]. Some cases were associated with surgical scars [ 114 ].…”

Section: Fibroblastic/myofibroblastic Tumoursmentioning

confidence: 99%

Mesenchymal tumours of the mediastinum—part I

et al. 2015

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The mediastinum is an anatomically defined space in which organs and major blood vessels reside with surrounding soft tissue elements. The thymus is an important organ in the mediastinum, and many of the masses encountered in the mediastinum are related to this organ. Most neoplasms diagnosed in the mediastinum are epithelial tumours (thymomas and thymic carcinomas), lymphomas or germ cell tumours. In contrast, soft tissue tumours of the mediastinum are rare. In 1963, Pachter and Lattes systematically reviewed soft tissue pathology of the mediastinum, covering the hitherto described [2, 226, 227] In this review, based on the 2013 WHO classification of soft tissue tumours and the 2015 WHO classification of tumours of the lung, pleura, thymus and heart, we provide an updated overview of mesenchymal tumours that may be encountered in the mediastinum.

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Section: Fibroblastic/myofibroblastic Tumoursmentioning

confidence: 99%

Mesenchymal tumours of the mediastinum—part I

et al. 2015

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“…They represent only 0.03% of all neoplasms, and the annual incidence is approximately 1‐4 per million population 1 . Most cases occur between the ages of 15 and 60 years old and more common in women than in men 2 …”

Section: Review Of the Literaturementioning

confidence: 99%

“…Desmoid tumors are locally aggressive and have a high rate of recurrence despite resection, but they do not metastasize 2 …”

Section: Review Of the Literaturementioning

confidence: 99%

Mitral regurgitation due to a mediastinal desmoid tumor: A case report and review of the literature

Shebli

Alzahran

Mansour

et al. 2020

Clinical Case Reports

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Desmoid tumors are rare benign tumors that arise most commonly in the abdomen, but can occasionally appear in extra-abdominal sites. We present a 3-year-old girl with mitral regurgitation in whom the final diagnosis was a mediastinal desmoid tumor. We managed the patient with complete surgical resection with an uneventful follow-up. Desmoid tumors are rare benign soft-tissue tumors that consist of proliferated, well-differentiated fibroblasts. They represent only 0.03% of all tumors, and their incidence is between 1 and 4 per million population annually. 1 Most patients are between 15 and 60 years old, and they affect women more commonly than men. 2 Desmoid tumors are locally aggressive and often recur even after complete resection, but they do not metastasize. 2 Desmoid tumors most commonly arise in the abdomen, but can occasionally appear in extra-abdominal sites such as chest wall, shoulder, mediastinum, and other rare sites. 3 We report a case of a 3-year-old girl with a mediastinal desmoid tumor and a thorough review of the literature to summarize the characteristics of mediastinal desmoid tumors. 2 | CASE PRESENTATION A 3-year-old girl presented to the hospital with a 4-month history of dry cough and dyspnea. Her past medical and surgical history was unremarkable. On physical examination, there was mild-to-moderate dyspnea without cyanosis or pallor. Chest examination showed diminished breath sounds on the right side with a respiratory rate of 44/min and an oxygen saturation of 95%. Heart rate was 136/min, blood pressure was 100/70 mm Hg, and there was a pansystolic murmur heard in the mitral area graded 3/6. The abdomen was tender, and the liver was displaced inferiorly about 6 cm below the costal margin without splenomegaly or venous dilations on the abdominal wall. Laboratory tests revealed abnormal levels of CRP (8 mg/L), ESR (31 mm/h), K + (3.4 mmol/L), and urea (32 mg/dL). Other laboratory tests, including tumor markers, were unremarkable. Chest X-ray (CXR) revealed a homogeneously increased density over the entire right side of the chest, shifting the mediastinum to the left, as seen in Figure 1.

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