Partial anomalous pulmonary venous connection and pulmonary arterial hypertension

Sahay, Sandeep; Krasuski, Richard A.; Tonelli, Adriano R.

doi:10.1111/j.1440-1843.2012.02180.x

Cited by 40 publications

(30 citation statements)

References 24 publications

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“…Agitated saline is used to aid the diagnosis by echocardiography but a PAPVC may get overlooked. A PAPVC may be mistakenly diagnosed as ASDs if the observer is not conscious about the fact that a PAPVC may be present with an intact atrial septum, and in these cases the intervention is not required if the patient is not symptomatic [3].…”

Section: Discussionmentioning

confidence: 99%

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A rare case of Abmormal Connection of Right Inferior Pulmonary Vein to Right atrium with Intact Intera trial Septum

Kalita¹,

Saikia²,

Sharma³

et al. 2016

SJAMS

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Isolated Partial Anomalous Pulmonary Venous Connection is a rare congenital defect that may not clinically manifest until adulthood. It can be misdiagnosed as a secundum type atrial septal defect by an echo cardiographer too. We present a 9 year-old girl who presented to us with complaints of occasional exertional fatigue. An ejection systolic murmur was heard in the 2 rd inter-costal space at left parasternal area. The cardiothoracic ratio was normal in routine chest X-ray with an anomalous vessel adjacent to the left pulmonary hilum. Echocardiography revealed an ostium secondum type of atrial septal defect of 18x10 mm in size with absence of inferior limb. She was taken up for surgery for closure of atrial septal defect. Intraoperatively, it was found that the atrial septum was intact but the right inferior pulmonary vein was draining to the right atrium. Surgically the defect was corrected by resecting part of atrial septum and tunneling the right inferior pulmonary vein to left atrium with a Dacron patch. The postoperative outcome was uneventful.

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Section: Discussionmentioning

confidence: 99%

“…PAPVC is found in around 0.4-0.7% of autopsies [3]. Anomalous pulmonary venous connection occurs in approximately 10-15% of ostium secundum ASD and 85 % of patients with sinus venosus ASD [3].…”

Section: Introductionmentioning

confidence: 99%

A rare case of Abmormal Connection of Right Inferior Pulmonary Vein to Right atrium with Intact Intera trial Septum

Kalita¹,

Saikia²,

Sharma³

et al. 2016

SJAMS

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“…Partial anomalous pulmonary venous return (PAPVR) is commonly associated with approximately 85% of sinus venosus and 10% to 15% of ostium secundum ASD cases (Fig. 1) [7].…”

Section: Assessment Of Complex Congenital Heart Diseasementioning

confidence: 99%

“…Partial anomalous pulmonary venous return (PAPVR) is commonly associated with approximately 85% of sinus venosus and 10% to 15% of ostium secundum ASD cases (Fig. 1) [7].Congenitally corrected transposition of the great arteries (ccTGA) is a rare congenital heart disease with atrioventricular and ventriculoarterial discordance. Ventriculoarterial discordance indicates that the morphological right ventricle connects to the aorta, and the morphological left ventricle connects to the pulmonary artery (Fig.…”

mentioning

confidence: 99%

Non-Coronary Findings on Cardiac Computed Tomography in Adults: What Radiologists Should Know

Lee

Ahn

et al. 2017

Cardiovasc Imaging Asia

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INtroductIoNRecent advances in technology have made cardiac computed tomography (CT) a useful tool for detection of coronary artery disease. Several studies using 64-slice CT demonstrated high sensitivity (96-99%) and a negative predictive value (93-99%) of cardiac CT in excluding significant coronary artery disease [1][2][3]. Therefore, cardiac CT can act as a gatekeeper to invasive coronary angiography. In addition, the appropriateness criteria for cardiac CT published by the American College of Cardiology list various non-coronary applications [4]. These include evaluation of 1) complex congenital heart disease, 2) cardiac masses, 3) pericardial conditions, 4) pulmonary vein anatomy prior to invasive radiofrequency ablation (RFA) in atrial fibrillation, 5) noninvasive coronary vein mapping prior to placement of a biventricular pacemaker, 6) suspected aortic dissection or thoracic aortic aneurysm, and 7) suspected pulmonary embolism. In this article, we will review the non-coronary application of cardiac CT and demonstrate typical CT case findings in adults. Because non-electrocardiogram (ECG)-gated CT is usually sufficient to assess a thoracic aortic aneurysm or pulmonary embolism, we excluded these conditions in this pictorial essay. AssessmeNt of complex coNgeNItAl heArt dIseAseCardiac CT can simultaneously provide information about the great vessels, cardiac chambers, and valve anomalies, with excellent spatial resolution and fast acquisition time in adult congenital heart disease [5].Atrial septal defect (ASD) is the most common congenital heart disease. Among the four subtypes of ASD, ostium secundum ASD is the most common (70-80%), followed by ostium primum ASD (15%), sinus venosus ASD (10%), and coronary sinus ASD (<1%) [6]. Cardiac CT can help to evaluate ASD and its subtypes, measure a defect or rim size, and assess a combined anomaly. In most cases of ostium primum ASD, the anterior leaf of the mitral valve is cleft. Partial anomalous pulmonary venous return (PAPVR) is commonly associated with approximately 85% of sinus venosus and 10% to 15% of ostium secundum ASD cases (Fig. 1) [7].Congenitally corrected transposition of the great arteries (ccTGA) is a rare congenital heart disease with atrioventricular and ventriculoarterial discordance. Ventriculoarterial discordance indicates that the morphological right ventricle connects to the aorta, and the morphological left ventricle connects to the pulmonary artery (Fig. 2). This double discordance results in physiologically corrected circulation, with the morphological left ventricle supplying the pulmonary circulation, and the cc This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/bync/4.0) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited. Cardiac computed tomography (CT) is useful for the assessment of both non-coronary cardiac disease and coronary artery disease...

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“…1 Rarely, PAPVC can present as an isolated cause of pulmonary hypertension. 2,3 We are reporting a case of 18 years old female who presented with effort intolerance. Investigations revealed the presence of obstructive PAPVC being the underlying etiology for pulmonary hypertension in this case.…”

Section: Introductionmentioning

confidence: 99%

Pulmonary hypertension due to presence of isolated partial anomalous pulmonary venous connection: A case report

Kumar

Patra

Ramalingam

et al. 2014

Journal of Cardiovascular Disease Research

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a b s t r a c tAnomalous pulmonary venous return is an uncommon congenital malformation which can be broadly categorized into partial or total, of which the former is more common. The anomaly is considered to be partial if some of the pulmonary veins drain into the systemic circulation and total if all the pulmonary veins drain into systemic circulation. Isolated partial anomalous pulmonary venous return (PAPVC) is an uncommon finding and is a very uncommon cause of pulmonary arterial hypertension. Whilst many patients with PAPVC remain asymptomatic, some may present at a later age with symptoms related to left-to-right shunt, pulmonary hypertension and right heart failure. We are presenting an interesting case report of an 18 years old patient who presented with exertional dyspnea and fatigue conforming to NYHA class II symptom status. Trans-esophageal echocardiography revealed isolated obstructive PAPVC as the cause for pulmonary hypertension without other demonstrable left-to-right shunts.

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Partial anomalous pulmonary venous connection and pulmonary arterial hypertension

Cited by 40 publications

References 24 publications

A rare case of Abmormal Connection of Right Inferior Pulmonary Vein to Right atrium with Intact Intera trial Septum

A rare case of Abmormal Connection of Right Inferior Pulmonary Vein to Right atrium with Intact Intera trial Septum

Non-Coronary Findings on Cardiac Computed Tomography in Adults: What Radiologists Should Know

Pulmonary hypertension due to presence of isolated partial anomalous pulmonary venous connection: A case report

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