Pentalogy of Cantrell Associated With Thoracoabdominal Ectopia Cordis

Gao, Zhan; Duan, Qun-Jun; Zhang, Zewei; Ying, Liyang; Ma, Li

doi:10.1161/circulationaha.108.811000

Cited by 15 publications

(18 citation statements)

References 5 publications

Supporting

Mentioning

Contrasting

Unclassified

Order By: Relevance

“…However, mortality is still high for the complex surgeries done for highly severe cases. 4 In summary, we have demonstrated a complete case of pentalogy of Cantrell with clinical and state-of-the-art MDCTA imaging. MDCTA with 3-dimensional volume rendering and maximum-intensity projection postprocessing techniques can be highly useful in accurate pretreatment assessment of the complex anomalies associated with pentalogy of Cantrell.…”

Section: Liu Et Al Mdct Of Pentalogy Of Cantrell 1619mentioning

confidence: 77%

“…Because the prognosis depends on the severity of the pentalogy of Cantrell, precise anatomic description is mandatory; however, the patient with pentalogy of Cantrell will eventually die without surgery. 4 Management is surgical, consisting of palliative repair of the ventral hernia and diaphragmatic defect and palliative or corrective repair of the cardiovascular anomalies. However, mortality is still high for the complex surgeries done for highly severe cases.…”

Section: Liu Et Al Mdct Of Pentalogy Of Cantrell 1619mentioning

confidence: 99%

See 1 more Smart Citation

Multidetector Computed Tomographic Angiography Imaging of Pentalogy of Cantrell

et al. 2014

View full text Add to dashboard Cite

Figure. A, Clinical picture of the patient reveals large ventral herniation of the heart into lower chest and upper abdomen (arrow) along with ventral bowel herniation through the umbilicus (arrowhead) suggestive of omphalocele. B, Echocardiogram through the ectopia cordis demonstrates overlap of ascending aorta (aAO) with small-caliber partially visualized main pulmonary artery (mPA) arising from the ventricle. C, Sagittal 3-dimensional volume-rendered computed tomographic image reveals lower sternum defect (arrowhead), ventral ectopia cordis (bold arrow), and an omphalocele (thin arrow). D and E, Maximum-intensity projection (D) and volume-rendered images (E) demonstrate ventrally herniated single ventricle (SV) with rightward apex, giving rise to tetralogy of Fallot-type conotruncus and diffusely hypoplastic main pulmonary artery, which branches into the hypoplastic right pulmonary artery (triangular arrowhead) with absent left pulmonary artery originating from undersurface of aortic arch (thin arrow) by way of patent ductus arteriosus (bold arrow). Note patent ductus arteriosus (bold arrow) extending between the inferior aspect of aortic arch and the left pulmonary artery (thin arrow). Additional findings include aberrant right subclavian artery (short arrowhead) from the proximal descending aorta.by guest on

show abstract

Section: Liu Et Al Mdct Of Pentalogy Of Cantrell 1619mentioning

confidence: 77%

Section: Liu Et Al Mdct Of Pentalogy Of Cantrell 1619mentioning

confidence: 99%

Multidetector Computed Tomographic Angiography Imaging of Pentalogy of Cantrell

et al. 2014

View full text Add to dashboard Cite

show abstract

“…In humans, ectopia cordis may be related to the quintet syndrome; abdominal wall, sternum, diaphragm, pericardium and heart defect, mostly described as Cantrell's pentalogy [7,15,16] . Unusual defects together with ectopia cordis may be also observed in calves.…”

Section: Discussionmentioning

confidence: 99%

Ectopia Cordis Cervicalis and Its Surgical Treatment in A Holstein Calf

Özer¹,

Aydin²,

Güzel³

et al. 2014

Kafkas Univ Vet Fak Derg

View full text Add to dashboard Cite

Ectopia cordis is a rare congenital anomaly characterized by partial or complete displacement of the heart, outside the thoracic cavity. Ectopia cordis is usually associated with other multiple anomalies and intra-cardiac defects due to developmental problems in the ventral body wall. In this report, a 6 day-old, 55 kg male Holstein calf with a case of ectopia cordis cervicalis and its surgical treatment has been presented. Following examinations (clinical, haematological, ECG, x-ray, USG and CT) a single staged surgery was performed to correct localisation of the heart in the thoracic cavity. The case was followed up 10 days postoperatively. However, the calf died at the end of post-operative day 10 due to septic shock. Keywords: Calf, Ectopia cordis cervicalis, Congenital abnormality Holstein Irkı Bir Buzağıda Ectopia Cordis Cervicalis Olgusu ve Operatif Sağaltımı ÖzetEctopia Cordis, kalbin göğüs kafesi dışında, parsiyal ya da tam olarak anormal yerleşimiyle karakterize, seyrek rastlanan kongenital bir anomalidir. Ectopia cordis, ventral karın duvarının gelişimindeki problemlere bağlı olarak genellikle intrakardiyak defektlerle ya da diğer çoklu anomalilerle ilişkili olabilir. Bu makalede, 6 günlük, erkek, 55 kg ağırlığında, Holstein bir buzağıda görülen ectopia cordis cervicalis olgusu ve operatif sağaltımı anlatılmaktadır. Yapılan muayeneler (klinik, hematolojik, EKG, radyografik, ultrasonografik, BT) sonucunda hastaya, kalbin göğüs kafesi içine alınmasına yönelik olarak tek seansta, cerrahi sağaltımda bulunuldu. Hastanın, 10 gün süreyle postoperatif takibi yapıldı fakat buzağı 10. günün sonunda septik şok nedeniyle öldü.

show abstract

“…9B), therefore, might or might not be associated with this syndrome. 20,42,46,47,52 Often the full spectrum of the PC is not complete 45 and therefore the following classification was proposed: complete syndrome (all 5 defects present), probable syndrome (4 defects present, including midline supraumbilical abdominal wall and structural intracardiac abnormalities), and incomplete syndrome (multiple combinations of abnormalities, although necessarily including a sternal abnormality). 53 Almost all patients have ventricular septal defects; other common intracardiac defects include atrial septal defect (53%), valvular or infundibular pulmonary stenosis (33%), tetralogy of Fallot (20%), and left ventricular diverticulum (20%).…”

Section: Ectopia Cordis and Pcmentioning

confidence: 99%