Percutaneous coil embolisation of congenital hepatic arteriovenous malformations in two patients with congenital heart disease and review of the literature

Abstract

Congenital hepatic arterio-venous malformations (AVM) are rare vascular anomalies and have rarely been reported in the presence of congeni-tal heart disease. The reported cases are mostly hemangiomas fed either by the hepatic artery itself or by one of its branches. We present two unique hepatic AVM cases in the presence of congenital heart defects in which the AVM was not fed by the hepatic arterial system. Transcatheter coil embolisation was successfully carried out in both of them by using non-detachable Gianturco coils. Complete occlusion was achieved without any sequel

A Massive Arteriovenous Malformation arising from the Aorta causing Severe Pulmonary Hypertension

“…These vascular malformations occur due to dysregulation in morphogenetic vascular development [2]. The most common site for neonatal vascular malformations is the liver, followed by the brain and lung [3]. Diagnosis of AVMs can be difficult in the neonatal period as their clinical presentation is very variable [4].…”

Retroperitoneal Arteriovenous Malformation: A Rare Cause of Pulmonary Hypertension in a Premature Infant

“…The currently available classification of the International Society for the Study of Vascular Anomalies (ISSVA) defines arteriovenous malformation (AVM) as nidus containing fast flow network of dysplastic arteries and veins [1]. The most frequent location of AVMs in neonates is liver, whereas lung and brain AVMs are silghtly less common [2]. Diagnosis can be complicated at birth as the clinical features of AVMs are variable and may occur with a long latency period.…”