“…The fact that our only case with supralevator rectal agenesis (patient 3) had vertebral and renal malformations further reinforces this concept. Immediate repair by simply opening the PC with or without excision of the remaining mucosa [2,4,6] or perineal fistulectomy [4,10 -12] are probably the best approaches in most of the simpler cases, but whenever in doubt about the anatomy, a sigmoidostomy should be performed in order to allow for a more accurate diagnosis and planning of a more appropriate surgical approach [3, 4, 7,11 -13]. The operation itself cannot be considered a simple one [2], at least in some cases.…”