Peripheral pulmonary artery stenosis.

Salisbury, D M; Keeling, Jean W.

doi:10.1136/adc.53.5.428

Cited by 5 publications

(2 citation statements)

References 3 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…Developmental origin: D1, D3, PD. PPS associated with William’s syndrome has been documented in patients aged < 5 weeks, 169 , 170 and PPS of undefined association shortly after birth 36 , 171 indicating likely in utero development, but progression can occur later. 41 , 171 , 172 …”

Section: Types Of Ph: Rationale For Assignment Of Characteristicsmentioning

confidence: 99%

“…30 Intimal thickening, fibromyxomatous or cellular, [30][31][32][33][34] is the most consistent finding. Also observed is medial hyperplasia, 30,35 paucity or fragmentation of medial elastic fibers and mosaic pattern of medial elements, 30,31,[33][34][35][36] and dilation with medial atrophy distal to areas of narrowing. 31,33 Hypoplasia of central PAs, with normal intima, media, and adventitia, has also been observed.…”

Section: Histopathological Typesmentioning

confidence: 99%

See 1 more Smart Citation

Pulmonary hypertension’s variegated landscape: a snapshot

Kulik

Austin

2017

Pulm. circ.

View full text Add to dashboard Cite

The many types of pulmonary hypertension (PH) are so protean in their biological origin, histological expression, and natural history that it is difficult to create a summary picture of the disease, or to easily compare and contrast characteristics of one type of PH with another. For newcomers to the field, however, such a picture would facilitate a broad understanding of PH. In this paper, we suggest that four characteristics are fundamental to describing the nature of various types of PH, and that taken together they define a number of patterns of PH expression. These characteristics are histopathology, developmental origin, associated clinical conditions, and potential for resolution. The “snapshot” is a way to concisely display the ways that these signal characteristics intersect in select specific types of PH, and is an effort to summarize these patterns in a way that facilitates a “big picture” comprehension of this disease.

show abstract