Introduction. Hairy polyp is a rare malformation which consists of mesodermal and ectodermal elements. It is the most common congenital nasopharyngeal tumour. The clinical symptoms depend on the size and localization of the mass. Early surgical excision results in permanent cure. Case report. The child was born from regularly controlled pregnancy. Prenatally, in the 24th week of gestation, epulis gigantocellularis was suspected, magnetic resonance imaging confirmed existence of protruding mass. Immediately after the birth, a tissue formation connected with the hard palate was observed protruding out of the mouth, as well as split of soft palate and tongue. In the first day of life the child was intubated and a mechanical ventilatory support started. In the fourth day of life, tracheostomy was performed. In the 40th day of life, the tumor mass was entirely excised with the reconstruction of the existing deformity of the mouth. The histopathological analysis confirmed the diagnosis of hairy polyp. In the fifth month of life, a percutaneous endoscopic gastrostomy was placed. At the beginning of the second age, the split of tongue and soft palate was sewn. With the establishment of normal swallowing, decannulation and closing of tracheostomy were performed and then gastrostomy was closed. Conclusion. Although the hairy polyp is a rare tumor, it must be included in the differential diagnosis of pharyngeal mass in the neonatal period. If there are no associated anomalies and if complete surgical resection of the tumor is performed, further course of the treatment will be favourable.