Physical fitness in children with haemophilia and the effect of overweight

Riet, D. C. M. Douma-Van; Engelbert, R. H. H.; Genderen, Frank R. Van; Ronde, Manon T. M. Ter Horst-De; Goede-Bolder, Arja de; Hartman, Annelies

doi:10.1111/j.1365-2516.2008.01928.x

Cited by 50 publications

(92 citation statements)

References 19 publications

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“…Besides the finding that a larger AROM was associated with a lower physical appearance, no associations were found between joint status (pain and range of motion) and perceived competence. In addition, a high perceived impact of (7)(8)(9)(10)(11)(12)(13)(14)(15)(16)(17)(18)(19)(20) 16.6 (2.9) Global self-worth 18.9 (4.0)* Range (11)(12)(13)(14)(15)(16)(17)(18)(19)(20)(21)(22)(23)(24) 20.0 (3.0) 15.7 (2.8) Range (9)(10)(11)(12)(13)(14)(15)(16)(17)(18)(19)(20) 16.0 (2.7) SD, standard deviation; SPPC, Self Perception Profile for Children; SPPA, Self Perception Profile for Adolescents. *P < 0.05, comparisons based on confidence interval analysis.…”

Section: Impact Of Diseasementioning

confidence: 98%

Perceived competence in children and adolescents with haemophilia: an explorative study

Hegeman¹,

Genderen²,

Meijer³

et al. 2010

Haemophilia

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With the introduction of prophylaxis, restricting children with haemophilia to participate in physical activities was no longer necessary. Subsequently, many studies report on improved physical functioning in children and adolescents with haemophilia. However, little is known about psychological aspects such as perceived competence and impact of disease. Therefore, the aims of this study were to explore: (i) perceived competence, (ii) perceived impact of illness, and (iii) analyse associations between perceived competence and demographic factors, disease-related factors and joint status in young haemophiliacs in the Netherlands. Fifty-four children (age 8-12 years) and 72 adolescents (12-18 years) with haemophilia participated in this cross-sectional, multi-centre, explorative study. Measurements included perceived competence (Self Perception Profile for Children/Adolescents; range 6-24/5-20), impact of disease (Revised Perception Illness Experience; range 1-5), demographic factors, disease-related factors, joint status and functional status. Mean (SD) scores for perceived competence in the children ranged from 17.3 (±4.0) to 19.6 (±4.0), and for adolescents from 13.3 (±2.4) to 15.7 (±2.8) points. In general, scores were comparable with those of healthy peers, but children with haemophilia had a lower global self-worth score and competence in close friendship was lower for adolescents when compared with those of healthy peers. Mean (SD) scores for impact of disease ranged from 1.2 (±0.4) to 2.3 (±0.8) in children and from 1.3 (±0.4) to 2.0 (±0.8) in adolescents. Severe haemophilia, prophylactic medication, high impact of disease and a shorter walking distance showed a weak to moderate association with perceived competence. Children and adolescents with haemophilia in general have a perceived competence that is nearly comparable with that of healthy peers, with the exception of a lower global self-worth in children and a lower competence for close friendship in adolescents. Haemophiliacs seem to perceive their disease as having relatively low impact on their life. Severe disease, prophylactic treatment and low functional status seemed to be associated with lower perceived competence.

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Section: Impact Of Diseasementioning

confidence: 98%

Perceived competence in children and adolescents with haemophilia: an explorative study

Hegeman¹,

Genderen²,

Meijer³

et al. 2010

Haemophilia

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“…Stephensen et al [7,14] 3DGA: as previously described Ground reaction forces normalized to body mass (N kg À1 ) and joint moments incorporating magnitude and direction and normalized to body mass (Nm kg À1 ) 6-Minute walk test (6MWT) Douma-van Riet et al [15] Hassan et al [16] Walk as far as possible in 6 min around a set course Distance walked (m)…”

Section: Kinetic Gait Patternsmentioning

confidence: 99%

“…Schoenmakers et al [18] Engelbert et al [20] Douma-van Riet et al [15] Koiter et al [21] Tiktinsky et al [22] Hand-held myometera portable force transducer records the amplitude of force produced by an isometric (static) muscle contraction…”

Section: Maximal Muscle Strengthmentioning

confidence: 99%

Outcome measures monitoring physical function in children with haemophilia: a systematic review

2013

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Our objective was to provide a synthesis of measurement properties for performance-based outcome measures used to evaluate physical function in children with haemophilia. A systematic review of articles published in English using Medline, PEDro, Cinahl and The Cochrane Library electronic databases was conducted. Studies were included if a performance-based method, clinical evaluation or measurement tool was used to record an aspect of physical function in patients with haemophilia aged ≤ 18 years. Recording of self-perceived or patient-reported physical performance, abstracts, unpublished reports, case series reports and studies where the outcome measure was not documented or cross-referenced was excluded. Description of outcome measures, patient characteristics, measurement properties for construct validity, internal consistency, repeatability, responsiveness and feasibility was extracted. Data synthesis of 41 studies evaluating 14 measures is reported. None of the outcome measures demonstrated the requirements for all the measurement properties. Data on validity and test-retest repeatability were most lacking together with studies of sufficient size. Measurement of walking and muscle strength demonstrated good repeatability and discriminative properties; however, correlation with other measures of musculoskeletal impairment requires investigation. The Haemophilia Joint Health Score demonstrated acceptable construct validity, internal consistency and repeatability, but the ability to discriminate changes in physical function is still to be determined. Rigorous evaluation of the measurement properties of performance-based outcome measures used to monitor physical function of children with haemophilia in larger collaborative studies is required.

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“…Investigaciones recientes muestran que los niños hemofílicos presentan menor resistencia aeróbica 55,56 , resistencia anaeróbica y fuerza [57][58][59] respecto de los valores encontrados en el resto de la población infantil. Sin embargo, otros estudios confirman niveles similares, tanto de capacidad aeróbica 60,61 , de fuerza 55,62 o de ambas 63,64 . Hoy en día, y a diferencia de los adultos, los niños hemofílicos que disfrutan de los beneficios del tratamiento hematológico tienen un buen equilibrio y propiocepción, además de disfrutar de una buena salud articular 55,59,61,62 .…”

Section: La Condición Física Del Paciente Hemofílicounclassified

“…Este hecho concuerda con la tendencia de la sociedad actual al sedentarismo, tanto en países desarrollados como en vías de desarrollo 48 . Esta tendencia al sedentarismo se ve reflejada en la presencia de sobrepeso y obesidad en la población hemofílica, detectada en numerosos estudios, sobre todo con niños 55,63,[69][70][71] y en el incremento de su prevalencia durante los últimos años. Este incremento, aunque similar al de la población no hemofílica, es alarmante, ya que el sobrepeso y la obesidad tienen un profundo efecto en la morbilidad y calidad de vida, agravando la artropatía preexistente y predisponiendo a enfermedades cardiovasculares 71 .…”

Section: La Condición Física Del Paciente Hemofílicounclassified

Hemofilia: ejercicio y deporte

Querol

Pérez‐Alenda

Gallach

et al. 2011

Apunts. Medicina de l'Esport

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Resumen El ejercicio físico y el deporte constituyen uno de los pilares básicos en el tratamiento de la hemofilia. Este trabajo describe un resumen de las características de la hemofilia y, a través de una exhaustiva revisión bibliográfica, se analiza la importancia de la condición física, en relación con la prevención y el tratamiento de las lesiones musculoesqueléticas en el paciente hemofílico.La hemofilia es una enfermedad hematológica hereditaria, con lesiones ortopédicas características. Afecta a individuos varones y presenta un déficit de factores de la coagulación que provoca hemorragias incluso espontáneas (en pacientes graves sin tratamiento). Las lesiones más frecuentes son: hemartrosis, sinovitis, hematomas musculares y artropatía hemofílica. La condición física del paciente hemofílico, instrumentada mediante terapia sustitutiva de factores de la coagulación, es fundamental y requiere fisioterapia, ejercicio físico y deporte.Basándonos en las recomendaciones de los comités de expertos de la Federación Mundial de Hemofilia (WFH) y utilizando las principales bases de datos, mediante estrategias de búsqueda con palabras clave, se obtuvieron 756 referencias, de las que tan sólo 74 superaron los criterios de inclusión.Las publicaciones se agruparon por áreas temáticas, diferenciando artículos de revisión, trabajos observacionales y experiencias clínicas, estudios experimentales y actuaciones intervencionistas sobre parámetros concretos de la condición física.Se concluye con la evidencia de la importancia de la recomendación del ejercicio físico y deporte en la hemofilia, el consenso en su idoneidad para el bienestar físico, psíquico y social de los pacientes, y la necesidad de incrementar los trabajos científicos al respecto. © 2010 Consell Català de l'Esport. Abstract Physical exercise and sports is one of the basic foundations in the treatment of haemophilia. This article gives a brief description of the characteristics of haemophilia, and through an exhaustive literature review, the importance of the physical condition, as regards prevention and treatment of musculoskeletal lesions in the haemophilic patient, is also analysed.Haemophilia is a hereditary haematological disease, characteristic orthopaedic lesions. It affects males and has a deficiency of clotting factors which causes haemorrhages, including spontaneous (in severe patients without treatment). The most common lesions are: haemarthrosis, synovitis, muscle haematomas and haemophilic arthritis. The physical condition of the haemophilic patient, controlled by clotting factor replacement therapy, is fundamental and requires physiotherapy, physical exercise and sport.Based on the recommendations by expert committees of the World Haemophilia Foundation (WFH) and using major data bases and search strategies with key words, 756 references were obtained, of which on 74 passed the inclusion criteria.The publications were grouped by subject area, differentiating review articles, observational studies and clinical experiences, experimental studies and ...

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Physical fitness in children with haemophilia and the effect of overweight

Cited by 50 publications

References 19 publications

Perceived competence in children and adolescents with haemophilia: an explorative study

Perceived competence in children and adolescents with haemophilia: an explorative study

Outcome measures monitoring physical function in children with haemophilia: a systematic review

Hemofilia: ejercicio y deporte

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