Pigmented Paravenous Chorioretinal Atrophy

ERG and EOG in progressive paravenous retinochoroidal atrophy

“…Patients with analogous fundus changes were described by several other authors (HsinHsiang, 1948;Archer, Krill and Ernest, 1972;Chisholm and Dudgeon, 1973;Francois and De Roucke, 1974;Pearlman et al, 1975Pearlman et al, , 1978and Skalka 1979). Noble and Carr (1983) reported the longest follow-up study of 21 years. In one of the most affected patients they recorded a normal electrooculogram (EOG); in another case the EOG was reduced.…”

Inflammatory pigmented paravenous retinochoroidal atrophy

“…However some authors suggest a congenital origin 9,11 and others a primary retinal degeneration. 1 Chen et al reported a case with bilateral macular coloboma, PPRA and negative laboratory examinations and he speculated that it was a developmental abnormality in nature. 12 Some reports suggest an inflammatory cause.…”

“…[1][2][3][4][5][6][7][8][9] This is an asymptomatic disease usually detected during routine ophthalmic examination. The condition is generally bilateral and young adults are most commonly affected.…”

Electroretinogram in Hereditary Retinal Disorders

“…The first cases were reported by Francessetti under various names, however, the author concluded that the term ''pigmented paravenous retinochoroidal atrophy'' best describes the condition (Franceschetti, 1962). Although it is not a generalized retinal disorder, the extent and degree of retinal involvement varies significantly between affected patients (Noble & Carr, 1983;Traboulsi & Maumenee, 1986). The disease is usually asymptomatic and diagnosed incidentally during routine fundoscopic examinations.…”