Pigmented villonodular synovitis of the knee in a 12-month-old girl

Abstract

A 12-month-old girl presented with a chronic localised mass on the knee, discomfort and gradually increasing right genu valgum. A diagnosis of pigmented villonodular synovitis was suggested by magnetic resonance imaging and confirmed at the time of surgical excision of the mass. The patient showed no recurrence after 3 years of follow up, and she required no further management. Pigmented villonodular synovitis should be considered in the differential diagnosis of chronic knee swelling in children.

Atypical presentation of pigmented villonodular synovitis: A case report

“…This is only the second reported case of PVNS in Saudi Arabia; the first reported case was of a 12-month-old girl with PVNS affecting the knee. [6] In the current case report, the patient had a relatively late-onset PVNS that affected the knee. The mean age of PVNS presentation is 33 (±13.1) years;[2] the patient in this report was likely in her forties when PVNS occurred.…”

Pigmented villonodular synovitis in pediatric population: review of literature and a case report

“…This study reviews and summarizes 29 articles, published between 1975 and 2016, in which 42 cases of pediatric PVNS were reported [ 3 , 5 – 32 ] (Table 1 ). Because of the impossibility to retrieve pediatric data, the articles representing mixed adult and pediatric cases were excluded from the review [ 34 ].…”

“…A localized intra-articular form of PVNS that causes mechanical symptoms, such as anterior knee pain, meniscal injury, and patellar dislocation has been reported in adult PVNS [ 35 – 39 ]. Mechanical symptoms are extremely rare in pediatric cases of PVNS [ 3 , 5 – 32 ]. Recurrent patellar dislocation is a rare presentation of PVNS that was previously only reported in adult cases [ 38 ].…”

“…The youngest patient reported with PVNS was 12 months old [ 5 ]. Knee involvement is common in pediatric PVNS, although other affected areas have been reported, such as the foot and ankle, elbow, hip, sacroiliac joint, and multiple joint involvements [ 3 , 5 – 32 ].…”

“…The youngest patient reported with PVNS was 12 months old [ 5 ]. Knee involvement is common in pediatric PVNS, although other affected areas have been reported, such as the foot and ankle, elbow, hip, sacroiliac joint, and multiple joint involvements [ 3 , 5 – 32 ]. Some authors have determined that there is no sex predilection in PVNS, while other reports have shown a male or female predominance [ 1 , 2 , 33 ].…”