“…Polysplenia syndrome with a variation of HA and the SMA is often diagnosed incidentally in patients by CT [14]. A limited number of articles were published in the literature, in which the HA originates from the SMA with heterotaxy syndrome, as in our case [3,[14][15][16]. In addition, the SMV was located on the left side of SMA, which is a suspicious finding in terms of intestinal malrotation.…”