Posttraumatic Epidural Haematoma in a child with severe haemophilia A – case study

Abstract

This paper presents the case of a 5-year-old child with severe haemophilia A treated for epidural bleeding into the CNS resulting from spine trauma. Every case of CNS trauma in children with haemophilia entails a high threat to life and limb, and as a priority requires factor VIII supplementation and further urgent diagnostics. Treating a child with CNS bleeding in the course of haemophilia requires the cooperation of a team of specialists, including a haematologist, radiologist, neurosurgeon, orthopedist and rehabilitation specialist. The treatment strategy in itself and selection of a conservative or surgical treatment method require an in-depth analysis. Supplementation treatment should be initiated immediately following the diagnosis of a head or spinal column injury, or after the onset of signs and symptoms indicating CNS bleeding.

Extra Dural Hematoma of the Dorso-Lumbar Region in a Hemophiliac: A Rare Entity

“…In the case of CNS trauma or suspected trauma in a hemophilia patient, supplementation treatment should be started immediately before performing imaging diagnostics. In the case of hemophilia A, the dose is selected so that the first seven days enable achievement of an activity level of 80 -100 IU/dL as the starting dose, followed by a maintenance dose of 50 IU/dL over the next 14 days [11]. The mainstay treatment of children with spinal cord hematoma in the course of hemophilia consists in the substitution of the deficient factor.…”

Difficulties in the diagnosis of meningitis – a challenging case of a child with head injury

“…The neurological evaluation of a child, especially in an emergency condition, is often very difficult and requires specific differential procedures [5]. The initial management and treatment can be complicated, especially in a case of patients with additional disorders [6].…”