Preface

Hakim, Alan J.; Keer, Rosemary; Grahame, Rodney

doi:10.1016/b978-0-7020-3005-5.00031-8

Cited by 8 publications

(15 citation statements)

References 0 publications

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“…Joint Hypermobility Syndrome/Ehlers-Danlos Syndrome-Hypermobility Type is one of the heritable connective tissue disorders showing symptom overlap with Marfans Syndrome, Osteogeneis Imperfecta, Chronic Fatigue Syndrome and Fibromyalgia (Hakim, Malfait, De Paepe, & Sahota, 2010). Joint Hypermobility Syndrome is considered to be synonymous with EDS-hypermobility type (Grahame, 2013; Tinkle et al, 2009).…”

Section: Joint Hypermobility Syndrome/ehlers-danlos Syndrome-hypermobmentioning

confidence: 99%

“…Recovery may be slow with a number of setbacks (Simmonds & Keer, 2007). A continuing cycle of inactivity leads to a downward spiral of fear of pain and movement, fear of falling and of going out, a loss of confidence and an inability to leave the house (Hakim et al, 2010; Simmonds & Keer, 2008). The knock on effect of this downward spiral is like a “domino effect”, resulting eventually in increasing physical impairment (Keer & Butler, 2010), impacting on mental well-being and leading to social isolation.…”

Section: Togetherness/isolationmentioning

confidence: 99%

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A humanisation approach for the management of Joint Hypermobility Syndrome/Ehlers-Danlos Syndrome-Hypermobility Type (JHS/EDS-HT)

Clark

Knight

2017

International Journal of Qualitative Studies on Health and Well

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Joint Hypermobility Syndrome/Ehlers-Danlos Syndrome—Hypermobility Type (JHS/EDS-HT) is a complex and multisystemic condition which significantly impacts on a person’s health and well-being and is challenging for health professionals (HPs) to manage. People with JHS/EDS-HT and HPs recognise the individual nature and the complexities of the condition. There is a requirement to understand the condition within the context of the individual human dimensions of illness and healing. The aim of this paper is to explore the management of this condition using a theoretical model referred to as the Humanisation Framework. It is suggested that using the philosophical dimensions of this framework will empower HPs and those with JHS/EDS-HT to work together to proactively manage this condition. The eight dimensions of the Humanisation Framework facilitate an experiential understanding of the person within their context and environment, providing a constructive adjunct to the evidence-based management of those with JHS/EDS-HT. The humanisation framework was developed for health and social care and uses the philosophy behind well-being and what makes well-being possible. This paper explores how HPs may use aspects of the framework to understand the condition and empower and motivate those with JHS/EDS-HT to be active participants in their own well-being.

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Section: Joint Hypermobility Syndrome/ehlers-danlos Syndrome-hypermobmentioning

confidence: 99%

Section: Togetherness/isolationmentioning

confidence: 99%

A humanisation approach for the management of Joint Hypermobility Syndrome/Ehlers-Danlos Syndrome-Hypermobility Type (JHS/EDS-HT)

Clark

Knight

2017

International Journal of Qualitative Studies on Health and Well

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“…They include the following.Referral to a physical therapy specialist is expected for all JHS-EDS-HT patients in order to identify the need for specialized intervention, choose the best suited sport/fitness activity, and educate the patient to “joint” health; extensive information for the physical therapist is summarized in Hakim et al [155]. …”

Section: Principles Of Managementmentioning

confidence: 99%

Ehlers-Danlos Syndrome, Hypermobility Type: An Underdiagnosed Hereditary Connective Tissue Disorder with Mucocutaneous, Articular, and Systemic Manifestations

Castori¹

2012

ISRN Dermatology

176

239

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Ehlers-Danlos syndrome, hypermobility type, constituting a phenotypic continuum with or, perhaps, corresponding to the joint hypermobility syndrome (JHS/EDS-HT), is likely the most common, though the least recognized, heritable connective tissue disorder. Known for decades as a hereditary condition with predominant rheumatologic manifestations, it is now emerging as a multisystemic disorder with widespread manifestations. Nevertheless, the practitioners' awareness of this condition is generally poor and most patients await years or, perhaps, decades before reaching the correct diagnosis. Among the various sites of disease manifestations, skin and mucosae represent a neglected organ where the dermatologist can easily spot diagnostic clues, which consistently integrate joint hypermobility and other orthopedic/neurologic manifestations at physical examination. In this paper, actual knowledge on JHS/EDS-HT is summarized in various sections. Particular attention has been posed on overlooked manifestations, including cutaneous, mucosal, and oropharyngeal features, and early diagnosis techniques, as a major point of interest for the practicing dermatologist. Actual research progresses on JH/EDS-HT envisage an unexpected link between heritable dysfunctions of the connective tissue and a wide range of functional somatic syndromes, most of them commonly diagnosed in the office of various specialists, comprising dermatologists.

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“…Concomitant medications can be started during the opiate withdrawal phase, for variable periods, to treat coexisting anxiety, psychological co-morbidity and provide long-term central analgesia such as antidepressants, benzodiazepines and clonidine. Figure 2 summarizes a suggested pharmacological approach to opiate withdrawal 14. The suggested protocol was useful in our patient, however close liaison with other disciplines, such as the pain management team, could be useful in improving outcomes.…”

Section: Discussionmentioning

confidence: 99%

Opioids and the Gastrointestinal Tract - A Case of Narcotic Bowel Syndrome and Literature Review

Farmer¹,

Ferdinand²,

Aziz³

2013

J Neurogastroenterol Motil

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The worldwide use of opiates is increasing yet there is little evidence that in long-term, non-cancer patients, they have an efficacious effect on functional outcomes and quality of life measures. Although it seems paradoxical, chronic opiate use may lead to a pro-nociceptive state. Mechanisms for the development of the hyperalgesic state include activation of the opiate bimodal regulatory systems, dynorphin and spinal cord glia. A potential consequence of chronic opiate usage is the development of narcotic bowel syndrome, which is characterized by chronic or intermittent colicky abdominal pain or discomfort that worsens after the narcotic effects of opiates wear off. It is likely that this is an under-recognized diagnosis. We describe here a case of 26-year old female who had visited our institution multiple times with intractable chronic abdominal pain in the context of normal findings on haematological, biochemical, metabolic, endoscopic and radiological investigations. She had been treated with a multitude of opioid agonists with escalating doses. A diagnosis of narcotic bowel syndrome was made. On elective admission her daily analgesic requirements were 150 µg/hr fentanyl, 100 mg oramorph and 400 mg tramadol (equating to 740 mg oral morphine/24 hr). A detoxification regimen was prescribed which included rapid opiate withdrawal couple with the commencement of methadone, lorazepam, clonidine and duloxetine. She was discharged opiate free, with no abdominal pain, 14 days after admission. Clinicians must be aware of narcotic bowel syndrome, which is often erroneously labelled as a functional gastrointestinal disorder, in patients who have been on long-term opiates.

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Preface

Cited by 8 publications

References 0 publications

A humanisation approach for the management of Joint Hypermobility Syndrome/Ehlers-Danlos Syndrome-Hypermobility Type (JHS/EDS-HT)

A humanisation approach for the management of Joint Hypermobility Syndrome/Ehlers-Danlos Syndrome-Hypermobility Type (JHS/EDS-HT)

Ehlers-Danlos Syndrome, Hypermobility Type: An Underdiagnosed Hereditary Connective Tissue Disorder with Mucocutaneous, Articular, and Systemic Manifestations

Opioids and the Gastrointestinal Tract - A Case of Narcotic Bowel Syndrome and Literature Review

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