Pregnancy Management and Outcome in ADAMTS13 Deficiency: A Case Report

Abstract

Thrombotic Thrombocytopenic Purpura (TTP) is a genetic hematological disorder which includes deficiency of "Von willebrand factor cleaving protease" along with severe thrombotic microangiopathy that leads to microangipathic hemolytic anemia. Several records are taken to justify the following disease at differential age, with variegated level of severity. Case of pregnant women of 25 years is studied in this following study, her blood parameters are screened and treatments are done, on the basis of it. The proposed outcome revealed that pregnant women face much higher risk at carrying the hereditary TTP. Proper screening has to be done of all the hematological units at the time of pregnancy, psychological screening is also equally important at that time.