Prenatal Diagnosis and Management of Ectopia Cordis: Varied Presentation Spectrum

Türkyilmaz, Gürcan; Avcı, Şahin; Sivrikoz, Tuğba Saraç; Erturk, Emircan; Altunoğlu, Umut; Turkyilmazlmaz, Sebnem Erol; Kalelioğlu, I.; Has, Recep; Yüksel, Atıl

doi:10.1080/15513815.2018.1556367

Cited by 13 publications

(13 citation statements)

References 24 publications

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“…PC is rare association of anomalies and can be challenging to manage. Prenatal diagnosis and careful assessment is essential for appropriate postnatal management [20,21]. A multidisciplinary team including pediatric surgery, cardiac and thoracic surgery is essential for optimal management [22,23,24,25,26].…”

Section: Discussionmentioning

confidence: 99%

Complete and Incomplete Pentalogy of Cantrell

Kylat

2019

Children

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Section: Discussionmentioning

confidence: 99%

Complete and Incomplete Pentalogy of Cantrell

Kylat

2019

Children

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“…27 Interestingly, all of these conditions are associated with decreased or absent fetal movement, further strengthening the association between fetal movement and overall umbilical cord length. Additional fetal anomalies associated with short umbilical cords include: limb-body wall complex (or body stalk anomaly), [28][29][30][31][32][33][34][35][36][37] and ectopia cordis, 38 with both the latter groups representing lethal fetal anomalies and the former considered a result of either spontaneous early amnion disruption, vascular disruption, or embryonic dysgenesis. 28 Short umbilical cords (<40 cm) in the absence of associated fetal anomalies have been associated with a significant increase in Cesarean and operative vaginal births (both forceps and vacuum deliveries).…”

Section: Umbilical Cord Morphometry Lengthmentioning

confidence: 99%

Current Perspectives of Prenatal Sonography of Umbilical Cord Morphology

Sherer¹,

Al-Haddad²,

Cheng³

et al. 2021

IJWH

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The umbilical cord constitutes a continuation of the fetal cardiovascular system anatomically bridging between the placenta and the fetus. This structure, critical in human development, enables mobility of the developing fetus within the gestational sac in contrast to the placenta, which is anchored to the uterine wall. The umbilical cord is protected by unique, robust anatomical features, which include: length of the umbilical cord, Wharton's jelly, two umbilical arteries, coiling, and suspension in amniotic fluid. These features all contribute to protect and buffer this essential structure from potential detrimental twisting, shearing, torsion, and compression forces throughout gestation, and specifically during labor and delivery. The arterial components of the umbilical cord are further protected by the presence of Hyrtl's anastomosis between the two respective umbilical arteries. Abnormalities of the umbilical cord are uncommon yet include excessively long or short cords, hyper or hypocoiling, cysts, single umbilical artery, supernumerary vessels, rarely an absent umbilical cord, stricture, furcate and velamentous insertions (including vasa previa), umbilical vein and arterial thrombosis, umbilical artery aneurysm, hematomas, and tumors (including hemangioma angiomyxoma and teratoma). This commentary will address current perspectives of prenatal sonography of the umbilical cord, including structural anomalies and the potential impact of future imaging technologies.

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“…Pentalogy of Cantrell is a complex syndrome of numerous fetal anomalies that should be borne in mind during the ultrasound evaluation of an omphalocele, sternal defects, ectopia cordis Since the pathology is also chromosomal based, the counselling should be done for future pregnancies as it can be challenging to manage. Therefore, prenatal diagnosis and careful assessment is essential for appropriate postnatal management [17,18] . Ultrasonography should always be the primary modality for diagnosis which gives an opportunity to parents to be adequately counseled regarding management options.…”

Section: Resultsmentioning

confidence: 99%

Early detection of pentalogy of cantrell by sonography

Mane¹,

Goyal²,

Joshi³

2020

Int. J. Radiol. Diagn. Imaging

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Pentalogy of Cantrell is a rare congenital condition with a thoraco-abdominal disruption showing five characteristics i.e. ectopia cordis and intracardiac anomalies; lower sternal defect; midline supraumbilical thoraco-abdominal wall defect; anterior diaphragmatic defect; defect of pericardium. Ultrasound can be used for its early and confirmatory diagnosis. This is a study of a rare case of Pentalogy of Cantrell based on sonography findings in a 23 year old primigravida presenting for routine antenatal check-up.

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Prenatal Diagnosis and Management of Ectopia Cordis: Varied Presentation Spectrum

Cited by 13 publications

References 24 publications

Complete and Incomplete Pentalogy of Cantrell

Complete and Incomplete Pentalogy of Cantrell

Current Perspectives of Prenatal Sonography of Umbilical Cord Morphology

Early detection of pentalogy of cantrell by sonography

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