Prenatal diagnosis of anomalous drainage of the right superior vena cava to the left atrium

Abstract

Anomalous drainage of the right superior vena cava to the left atrium, as an isolated abnormality, is a very rare form of congenital heart disease that causes postnatal hypoxemia. There is only one other case reported in the literature of this anomaly diagnosed prenatally. We describe a case of isolated right superior vena cava to the left atrium diagnosed prenatally by our fetal cardiology team after obstetrical referral for a dilated superior vena cava, and we discuss the differential diagnosis of in utero dilation of the superior vena cava.