Priapism in an Infant With Sickle Cell Trait After Cardiac Transplant

Catastrophic sickling crisis in patient undergoing cardiac transplantation with sickle cell trait

“…In terms of cardiac transplantation in patients with sickle cell, there are only 2 adults and 1 child described who underwent cardiac transplantation with SCT, 1 of whom had a coexisting rare red cell membrane disorder . There are also case reports describing patients with SCD undergoing cardiac transplant .…”

“…Despite these challenges, there are several reports of successful outcomes for patients with SCD undergoing cardiac surgery, both with and without red cell exchange, including our center's experience of pulmonary endarterectomy with deep hypothermic circulatory arrest . In terms of cardiac transplantation, there are reports of only 2 adults and 1 child who underwent cardiac transplantation with SCT, and 1 adult and 6 children who underwent cardiac transplantation with SCD . Many heart transplant units that serve Afro‐Caribbean/African American populations do not specifically test for SCT during heart transplant assessment.…”

Priapism Among Male Adolescents with Sickle Cell Disease

“…This study also aimed to help society better understand the unique struggles that adolescent males with SCD and priapism face (Bacsu & Metcalfe, 2012). Understanding the physical pain and desperation of an adolescent male with chronic pain caused by SCD and persistent, uncomfortable erections may encourage society to support other SCD male adolescents dealing with priapism (Dampier et al, 2010).…”

“…The highest prevalence rates occur among Africans, Asians, and people of Mediterranean origin (Chrouser et al, 2011). This hemoglobin disorder, inherited from one's parents, is mainly characterized by vascular occlusion episodes, organ damage, and chronic hemolytic anemia, among other complications (Bacsu & Metcalfe, 2012). The United States has advanced in the management of the disorder through newborn procedures and prophylactic penicillin treatment of children with SCD (Bacsu & Metcalfe, 2012).…”

“…This hemoglobin disorder, inherited from one's parents, is mainly characterized by vascular occlusion episodes, organ damage, and chronic hemolytic anemia, among other complications (Bacsu & Metcalfe, 2012). The United States has advanced in the management of the disorder through newborn procedures and prophylactic penicillin treatment of children with SCD (Bacsu & Metcalfe, 2012). However, in some African countries that lack modern medical technology advancements, the estimated numbers of children born with SCD that die in early childhood are alarmingly high (Mulumba & Wilson, 2015).…”