Primary antiphospholipid antibody syndrome presenting as unilateral adrenal hemorrhage

Khare, Shruti; Patel, Hardik; Sutaria, Gargey; Sharma, Reena

doi:10.4103/ijem.ijem_474_17

Cited by 6 publications

(2 citation statements)

References 5 publications

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“…No previous history of thrombosis also made the diagnosis of APS challenging. Although uncommon, there have been reports of bilateral adrenal haemorrhage as the first presentation of APS 4,5 . It is possible that the patient's recent antecedent viral illness triggered his initial thrombotic manifestation of APS.…”

Section: Discussionmentioning

confidence: 99%

Abdominal pain secondary to bilateral adrenal haemorrhage as the first presentation of antiphospholipid syndrome

Wang

Nedumannil

Wolf

2023

Medical Journal of Australia

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Section: Discussionmentioning

confidence: 99%

Abdominal pain secondary to bilateral adrenal haemorrhage as the first presentation of antiphospholipid syndrome

Wang

Nedumannil

Wolf

2023

Medical Journal of Australia

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“…From another perspective, APS patients are typically in the hypercoagulable state. However, several conditions, such as hemorrhagic infarction after thrombosis formation, 26 anticoagulant therapy, pulmonary capillaritis, thrombocytopenia, thrombotic microangiopathies, or antibodies against prothrombin, could also appear in APS patients. Therefore, the major hemorrhage could occur in 10% of APS patients 27 .…”

Section: Discussionmentioning

confidence: 99%

Characteristics of Acquired Inhibitors to Factor VIII and Von Willebrand Factor Secondary to Systemic Lupus Erythematosus

Cao

Zhang

et al. 2019

J Clin Rheumatol

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ObjectiveBecause acquired hemophilia (AH) is a rare entity in systemic lupus erythematosus (SLE), we aimed to investigate the clinical features of SLE-related AH in Chinese patients.MethodsThis is a medical records review study carried out at a large tertiary care hospital in China from years 1986 to 2018. We searched the case database in Peking Union Medical College Hospital using the International Classification of Diseases. The clinical data on SLE-related AH patients were collected.ResultsA total of 9282 SLE patients had been hospitalized. Six female SLE-related AH patients were identified. Four patients had acquired hemophilia A (AHA), and 2 patients had acquired von Willebrand syndrome. Their mean age was 33.67 ± 13.77 years. Five patients had active disease. The mean SLE disease activity index measured at the time of diagnosis of AH was 10.50 ± 5.28. The average level of activated partial thromboplastin time was 86.5 seconds. Coexistence of secondary antiphospholipid syndrome and AHA was found in one case, and pulmonary embolism was observed 3 years later. After immunosuppressive therapy and symptomatic treatment, an overall remission rate of 83.3% was achieved.ConclusionsThe frequency of SLE-related AH was low. The development of AH in SLE patients frequently occurs with active disease. The AH could be the first clinical presentation of SLE. Secondary antiphospholipid syndrome and AHA could appear in the same SLE patient. Early and aggressive treatment contributes to a favorable prognosis.

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Spontaneous Adrenal Hemorrhage—a Mixed Bag: 18 Cases from a Single Institution

et al. 2019

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Primary antiphospholipid antibody syndrome presenting as unilateral adrenal hemorrhage

Cited by 6 publications

References 5 publications

Abdominal pain secondary to bilateral adrenal haemorrhage as the first presentation of antiphospholipid syndrome

Abdominal pain secondary to bilateral adrenal haemorrhage as the first presentation of antiphospholipid syndrome

Characteristics of Acquired Inhibitors to Factor VIII and Von Willebrand Factor Secondary to Systemic Lupus Erythematosus

Spontaneous Adrenal Hemorrhage—a Mixed Bag: 18 Cases from a Single Institution

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